TY  - JOUR
T1  - Panhipopituitarizm, hipotiroidi ve Noonan sendromlu pediatrik hastada anestezik yaklaşım: Olgu sunumu
TT  - Anesthetic management in a pediatric patient with Noonan syndrome, hypopituitarism and hypothyroidism: A case report
AU  - Yektaş, Abdulkadir
AU  - Altunbay, Ramazan Ahmet
AU  - Alagöl, Ayşin
PY  - 2013
DA  - June
DO  - 10.5799/ahinjs.01.2013.02.02275
JF  - Journal of Clinical and Experimental Investigations
JO  - J Clin Exp Invest
PB  - Aydın ECE
WT  - DergiPark
SN  - 1309-8578
SP  - 238
EP  - 241
VL  - 4
IS  - 2
LA  - tr
AB  - Noonan sendromu değişik patofizyolojik düzensizlikler ve değişik anatomik anomalilerle görülen, otozomal domi­nant genetik geçişle karakterize bir hastalıktır. Bu send­romla ilişkili anomaliler, hipertelorizm, pitozis, mikrognati, aşağı dönük palpebral fissürler, düşük yerleşimli-anormal heliksli kulaklar, derin oluklu filtrum, kısa ve/veya yele bo­yun, düşük ense saç çizgisi şeklinde dismorfik bulgulardır. Noonan sendromu tanısı almış hastalar zor hava yolu ile karşımıza çıkar. Trakeal entübasyon hava yolu ve servikal vertebral anomalilere ve maske ile ventilasyon asimetrik yüz yapısına bağlı olarak zor olabilir. Biz Noonan send­romlu bir olguya anestezik yaklaşımımızı sunmak istedik.
KW  - Anestezi
KW  - genel
KW  - noonan sendromu
KW  - hava yolu yönetimi
N2  - Noonan syndrome is a genetically transmitted autosomal dominant disorder characterized by various anatomic anomalies and pathophysiologic derangements. Associ­ated anomalies include hyperthelorism, ptosis, microgna­thia, downward sloping palpebral fissures, low-set ears, abnormal helix of ear, deeply grooved philtrum, short and/ or webbed neck, low hairline and cervical vertebral anom­alies. Patients with Noonan syndrome are known to pres­ent with challenging airways. Tracheal intubation can be difficult because of airway and cervical vertebral anoma­lies and bag mask ventilation may be difficult because of asymmetrical face. We present a case of anesthetic man­agement for Noonan syndrome. J Clin Exp Invest 2013; 4 (2): 238-241
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UR  - https://doi.org/10.5799/ahinjs.01.2013.02.02275
L1  - https://dergipark.org.tr/en/download/article-file/104161
ER  -