TY  - JOUR
T1  - Variants of systemic mastocytosis: A report of three cases
TT  - Sistemik mastositoz: Üç olgu sunumu
AU  - Sarı, İbrahim
AU  - Bahar, A. Yasir
AU  - Pehlivan, Mustafa
PY  - 2015
DA  - May
DO  - 10.5799/ahinjs.01.2015.01.0488
JF  - Journal of Clinical and Experimental Investigations
JO  - J Clin Exp Invest
PB  - Aydın ECE
WT  - DergiPark
SN  - 1309-8578
SP  - 65
EP  - 68
VL  - 6
IS  - 1
LA  - en
AB  - Advanced systemic mast cell neoplasms are very rare tumors and systemic mastocytosis is in the form of atypical leukemic infiltration of neoplastic mast cells to bone marrow and/or other organs. In this study, histological, immunohistochemical, flow cytometry, and molecular genetic findings of three patients that showing the increase in mast cells in the bone marrow discussed in terms of aggressive systemic mastocytosis, mast cell leukemia, systemic mastocytosis with associated clonal hematological non-mast lineage disease and myelomastocytic leukemia differential diagnosis in the light of the scientific literature. J Clin Exp Invest 2015; 6 (1): 65-68 Key words: Mast cell, neoplasm, differential diagnosis
KW  - Mast cell
KW  - neoplasm
KW  - differential diagnosis
N2  - İleri sistemik mast hücreli neoplaziler oldukça nadir tümörlerdir. Sistemik mastositoz, kemik iliği ve/veya diğer organlara neoplastik mast hücrelerinin atipik lösemik infiltrasyonu biçimindedir. Bu çalışmada kemik iliğinde mast hücre artışı gösteren 3 olgunun histolojik, immünohistokimyasal, flowsitometri ve genetik bulguları, ileri mast hücreli neoplazmlar -agresif sistemik mastositoz, mast hücreli lösemi, mast hücre dışı klonal hematolojik bir hastalıkla beraber olan sistemik mastositoz- ayırıcı tanısı açısından tartışılmıştır
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UR  - https://doi.org/10.5799/ahinjs.01.2015.01.0488
L1  - https://dergipark.org.tr/en/download/article-file/104480
ER  -