TY - JOUR T1 - A rare cause of Ortner’s syndrome: giant pulmonary artery aneurysm secondary to Behçet’s disease TT - Ortner sendromu’ nun nadir bir nedeni: Behçet hastalığına sekonder gelişen dev pulmoner arter anevrizması AU - Çelik, Abdullah AU - Karagöz, Ahmet AU - Seren, Erdal AU - Usta, Sefer AU - Vural, Aslı AU - Günaydın, Zeki AU - Bektaş, Osman PY - 2015 DA - May DO - 10.5799/ahinjs.01.2015.01.0489 JF - Journal of Clinical and Experimental Investigations JO - J Clin Exp Invest PB - Aydın ECE WT - DergiPark SN - 1309-8578 VL - 6 IS - 1 LA - en AB - Behçet’ s disease is a systemic autoimmune vasculitis of unknown etiology. It causes serious disability by affecting both arteries and veins. Hoarseness due to compression of the left recurrent laringeus nerve resulting from pathologies of the heart and intrathoracic great vessels is defined as Ortner’s syndrome. The most common cause of Ortner’s syndrome is left atrial enlargement due to mitral stenosis. Various intrathoracic pathologies may also be the reason. Beside, Ortner’s syndrome due to primary pulmonary artery aneurysm as a feature of Behçet’s disease is relatively rare. Herein, we report a case of a 78 year old female patient presenting with hoarseness and diagnosed as Ortner’s syndrome resulting from a giant pulmonary artery aneurysm secondary to Behçet’ s disease. J Clin Exp Invest 2015; 6 (1): 69-71 Key words: Ortner’ s Syndrome, Pulmonary Artery Aneurysm, Behçet’s Disease N2 - Behçet Hastalığı nedeni bilinmeyen sistemik bir otoimmün vaskülittir. Hem arterleri hem de venleri tutarak ciddi sorunlara neden olabilir. Kalp ve intratorasik büyük damarların patolojilerine bağlı olarak sol rekürren laringeal sinirin kompresyonu sonucu gelişen ses kısıklığı Ortner Sendromu olarak ifade edilir. Ortner Sendromu’ nun en sık nedeni mitral darlığa bağlı olarak sol atriyum genişlemesidir. Çeşitli intratorasik patolojiler bu tablonun nedeni olabilir. Bununla birlikte Behçet Hastalığı sonucu gelişen pulmoner arter anevrizmasına bağlı Ortner Sendromu nispeten nadirdir. Biz burada ses kısıklığı ile başvuran ve yapılan incelemeler sonucunda Behçet Hastalığı’ na bağlı dev pulmoner arter anevrizması sonucu gelişen Ortner Sendromu olarak tanı alan 78 yaşında bir bayan hastayı sunuyoruz CR - Türkcü FM, Yüksel H, Uçmak D, et al. Demographic characteristics CR - and ocular involvement in Behçet patients in CR - Southeast Anatolia. J Clin Exp Invest 2013;4:339-342. CR - Küçük A, Albayrak İ, Bağçacı S, Küçükşen S, Tunç R. CR - Upper extremity thrombosis in Behçet. Dicle Med J CR - ;40:507-509. CR - Tüzün H, Hamuryudan V, Yıldırım S, et al. Surgical therapy CR - of pulmonary arterial aneurysms in Behçet’s syndrome. CR - Ann Thorac Surg 1996;61:733-735. CR - Day JR, Walesby RK. A spontaneous ductal aneurysm CR - presenting with left recurrent laryngeal nevre palsy. Ann CR - Thorac Surg 2001;72:608-609. CR - Kokotsakis J, Misthos P, Athanassiou T, et al. Acute Ortner’s CR - syndrome arising from ductus arteriosus aneurysm. CR - Tex Heart Inst J 2008;35:216-217. CR - Shih HH, Kang PL, Lin CY, et al. Main pulmonary artery CR - aneurysm. J Chin Med Assoc 2007;70:453-455. CR - Imazio M, Cecchi E, Giammaria M, et al. Main pulmonary CR - artery aneurysm: a case report and review of the literature. CR - Ital Heart J 2004;5:232-237. CR - Subramaniam V, Herle A, Mohammed N, et al. Ortner’s CR - syndrome: case series and literature review. Braz J Otorhinolaryngol CR - ;77:559-562. CR - Mulpuru SK, Vasavada BC, Punukollu GK, et al. Cardiovocal CR - syndrome: a systematic review. Heart Lung Circ CR - ;17:1-4. CR - Sakuma M, Demachi J, Suzuki J, et al. Proximal pulmonary CR - artery aneurysms in patients with pulmonary CR - artery hypertension: Complicated cases. Intern Med CR - ;46:1789-1793. CR - Bartter T, Irwin R, Nash G. Aneurysms of the pulmonary CR - arteries. Chest 1988;94:1065-1075. CR - Smalcelj A, Brida V, Samarzija M, et al. Giant, dissecting, CR - high-pressure pulmonary artery aneurysm: CR - case report of a 1-year natural course. Tex Heart Inst J CR - ;32:589-594. CR - Graham JK, Shehata B. Sudden death due to dissecting CR - pulmonary artery aneurysm: a case report and review of CR - the literature. Am J Forensic Med Pathol 2007;28:342- UR - https://doi.org/10.5799/ahinjs.01.2015.01.0489 L1 - https://dergipark.org.tr/en/download/article-file/104481 ER -