TY  - JOUR
T1  - A neonatal lupus syndrome with pericardial tamponade due to maternal Sjögren’s syndrome
TT  - Maternal Sjögren sendromuna bağlı perikardiyal tamponadı olan neonatal lupus sendromu
AU  - Özdemir, Mustafa
AU  - Yapıcıoğlu, Hacer
AU  - Tepe, Tugay
AU  - Akbaş, Tolga
AU  - Özlü, Ferda
AU  - Erdem, Sevcan
PY  - 2023
DA  - July
Y2  - 2023
DO  - 10.17826/cumj.1241756
JF  - Cukurova Medical Journal
JO  - Cukurova Med J
PB  - Cukurova University
WT  - DergiPark
SN  - 2602-3032
SP  - 745
EP  - 747
VL  - 48
IS  - 2
LA  - en
AB  - Neonatal lupus syndrome (NLS) is a rare disease with dermatological, cardiac, hepatic and hematologic involvement due to placental transfer of anti-Ro/ SSA and anti-La/ SSB antibodies in infants of mothers with autoimmune diseases. Multisystemic involvement is common in infants. Here we present a baby with neonatal lupus syndrome whose mother had Sjögren's syndrome. He presented with thrombocytopenia, then convulsion and cardiac arrest due to pericardial tamponade. So, the risk of NLS should be kept in mind in infants of mothers with autoimmune diseases.
KW  - Sjögren’s syndrome
KW  - Neonatal lupus syndrome
KW  - Convulsion
KW  - Pericardial tamponade
N2  - Neonatal lupus sendromu (NLS), otoimmün hastalığı olan annelerin bebeklerinde anti-Ro/ SSA ve anti-La/ SSB antikorlarının plasental transferine bağlı olarak dermatolojik, kardiyak, hepatik ve hematolojik tutulumla seyreden nadir bir hastalıktır. Bebeklerde multisistemik tutulum sık görülür. Burada, annesinde Sjögren sendromu olan neonatal lupus sendromlu bir olgu sunulmuştur. Bebekte önce trombositopeni, ardından konvülsiyon ve perikardiyal tamponada ikincil kardiyak arrest gelişmiştir. Otoimmün hastalığı olan annelerin bebeklerinde NLS riski akılda tutulmalıdır.
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UR  - https://doi.org/10.17826/cumj.1241756
L1  - https://dergipark.org.tr/en/download/article-file/2914849
ER  -