TY  - JOUR
T1  - Cystic Fibrosis
TT  - KISTIK FIBROZIS
AU  - Kansu, Aydan
PY  - 1994
DA  - December
JF  - Ankara Üniversitesi Tıp Fakültesi Mecmuası
PB  - Ankara University
WT  - DergiPark
SN  - 0365-8104
SP  - 657
EP  - 666
VL  - 46
IS  - 4
LA  - en
AB  - Cystic fibrosis is an autosomal recessive inherited multisystem disease which manifests with exocrine gland functional deficiency.Previously it was regarded as an inherited fatal condition of infancy and childhood, recently due to advanced diagnostic methods and treatment modalities mean age of survival increased up to the twenties.As the prognosis depends mostly on pulmonary disease, the pediatrists and pulmonologists should be in cooperation in the Management and treatment of these patients.
KW  - Cystic fibrosis
KW  - NEONATOLOGY
KW  - CARDİOLOGY
N2  - Kistik Fibrozis otozomal ressesif kalitumla gecen ve ekzokrin bezlerin fonksiyon bozuklugu ile seyreden; cogul organ tutulumlu, dlimculbir hastaliktir. Eskiden yalnizca cocukluk déneminin hastaligi oldugu dustintlirken, giiniimtizde tani ve tedavi imkanlarinin artmasi ile ortalama yasam siiresi 20 yila ¢ikmustir, Hastaligin prognozunu daha cok pulmoner tutulum belirler. Bu nedenle hastalarin takiplerinde pediatrist ve gégiis hastahklar1 uzmanlannuin isbirlizi é6nem tasimaktadir.
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UR  - https://dergipark.org.tr/en/pub/autfm/issue//1721285
L1  - https://dergipark.org.tr/en/download/article-file/4966383
ER  -