TY - JOUR T1 - Peutz Jeghers Sendromu TT - Peutz-Jeghers Syndrome AU - Özden, Ali PY - 1986 DA - June JF - Ankara Üniversitesi Tıp Fakültesi Mecmuası PB - Ankara University WT - DergiPark SN - 0365-8104 SP - 207 EP - 213 VL - 39 IS - 2 LA - tr AB - Subileus ataklarıyla seyreden 13 yaşında Peutz Jeghers Sendromlu bir kadın hasta takdim edildi. İnce barsak ve kolon grafileri, gastro-intestinal endoskopi muayeneleri yapıldı. Mide, ince barsak ve kolonda polipler tesbit edildi. Barsak tıkanmasına yol açan büyük polip opere edildi ve hamartom polipi olarak tesbit edildi.Bu sendrom ailevi olup ağız çevresi deri, dudak ve yanak mukozasında bazı vakalarda eller ve ayaklarda küçük melanin pigmenti toplanmasıyla kendini gösterir. İnce barsakta subileus nede -i niyle kolik tarzında karın ağrısı ve kusmaya yol açabilir. Tümör 3 cm'den büyük olabilir ve bizim vakamızda olduğu gibi tıkanma semptomlarına sebep olabilir. KW - gastroenteroloji KW - makatta kan KW - vaka N2 - We report a case of Peutz-Jeghers Syndrome in a 13 years old female with subileus, Gastrointestinal x rays, gastrointestinal endos copic examination were done. She was found to have polyps in the stomach, small intestin, colon. Large polyp in the duodenume caused intestinal obstruction. She was operated. The polyp removed was hamartome. This syndrome is familial and usually recognized by the appearance of sınail melanotic spots on the perioral skin, lips, buccal mu- CR - I. Burdick Daniel, Prior TJ : Peutz-Jeghers Syndrome. A Clinicopathologic Study of a Large Family with a 27-Years Follow-up Cancer 50 : 2139-2146, 1982. CR - 2. Dozois RR et al : The Peutz Jeghers Syndrome. Is there a predisposition to the development in intestinal malignancy. Arch Surg 98 : 509-517, 1969. CR - 3. Godard JE, Dodds' WJ, Phillips JC : Peutz Jeghers Syndrome : Clinical and ro entgenopgraphic features. Am J Roentgenol 113 : 316-324, 1971. CR - 4, Jancu J Peutz Jeghers Syndrome Involvement of gastrointestinal and upper respiratory tracts. Am J Gastroenterol 56 545-549, 1971. CR - 5. Lehur AP et al : Peutz Jeghers Syndrome. Association of Duodenal and Bilateral Breast Cancers in the Same Patient Digestive Diseases and Sciences 29 178-181, 1984. CR - 6. Mc Kuskick VA : Genetic factors in intestinal poliposis JAMA 182 : 271-277, 1962. CR - 7. Riley E, Swift M : A family with Peutz Jeghers Syndrome and bilateral breast cancer. Cancer, 46 : 815-817, 1980. CR - 8. Sommerhang RG, Mason T : Peutz Jeghers Syndrome and ureteral polyposis.JAMA 311 : 120-122, 1970 CR - 9. Tovar AJB, Albert AE, Jimenez J : Pautz Jeghers Syndrome in Children : Report of Two Cases and Review of the Literature. Journal of Pediatric Surgery 18 : 1-6, 1983. CR - 10. Williams JP, Knudsen A : Peutz Jeghers Syndrome with Metastazizing duodenal carcinoma. Gut 6 : 179-184, 1965. UR - https://dergipark.org.tr/en/pub/autfm/issue//1725445 L1 - https://dergipark.org.tr/en/download/article-file/4983857 ER -