TY  - JOUR
T1  - Congenital Heart Disease in Down's Syndrome
TT  - Down Sendromunda Konjenital Kalp Hastalıkları
AU  - İmamoğlu, Ayten
PY  - 1979
DA  - December
JF  - Ankara Üniversitesi Tıp Fakültesi Mecmuası
PB  - Ankara University
WT  - DergiPark
SN  - 0365-8104
SP  - 479
EP  - 486
VL  - 29
IS  - 4
LA  - en
AB  - Eighty Down Syndrome cases were examined in our Pediatrics Department. Between the years 1972-1978. Twenty six of them (32.5%) were diagnosed as having congenital heart disease. The ratio of girls to boys Was 10 : 16 respectively. Eight patients (27 %) died because of congestive heart failure and respiratory diseases. Among the congenital heart diseases, Endocordial Cushion Defect “had the highest prevalance 42.3% -11 of the 26 patients. Ventricular Septal Defect (9 cases-34.6 %), Atrial Septal Defect (3 cases-11.5 %), Tetralogy of Fallot (2 cases-7.7 %) and Patent Ductus Arteriosus (1 cases-3.8 %) were following this respectively. Early diagnosis and surgical treatment will decrease mortality rate in these patients.
KW  - down syndrome
KW  - pediatrics
KW  - congenital heart diseases
N2  - 1972 - 1978 yılları arasında kliniğimizde görülen 80 Down sendromu olgusundan 26'sında konjenital kalp hastalığı saptandı. Oran  % 32.5 bulundu. Erkek- kız oranı 16/10 bulundu. Sekiz hasta (% 27) konjestif kalp yetmezliği ve akciğer hastalığı nedeni ile yitirildiler. Konjenital kalp hastalıkları arasında en olağan lezyon Endocardial Cushion Defect (11 olgu) % 42.3 olarak saptandı. Bunu sırası ile. ventriküler septal defekt (9 olgu) % 34.6, atrial septal defekt (3 olgu) % 11.5, Fallot tetralojisi (2 olgu) % 7.7 patent duktus arteriosus (1 olgu) % 3.8 izliyordu. Bizim araştırmamızdaki Down sendromu olgularında bulunan konjenital kalp hastalığı ve bunlar arasında major kalp lezyonlarının görülüş sıklığının literatürle uvgunluk gösterdiği saptandı. Erken cerrahi girişimin bu hastaların yaşamını uzatacağına dikkat çekildi.
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UR  - https://dergipark.org.tr/en/pub/autfm/issue//1732799
L1  - https://dergipark.org.tr/en/download/article-file/5014732
ER  -