TY - JOUR TT - Anesthetic management of pediatric patient with spinal muscular atrophy AU - Küçük, Ahmet AU - Yüce, Hasan Hüsnü AU - Aydoğan, Harun AU - Karahan, Mahmut Alp AU - Altay, Nuray PY - 2016 DA - April JF - Pamukkale Medical Journal JO - Pam Tıp Derg PB - Pamukkale University WT - DergiPark SN - 1308-0865 SP - 57 EP - 61 IS - 1 KW - Spinal Musküler Atrofi KW - Kaudal Anestezi KW - propofol N2 - Spinal muscular atrophies, are a group of mostly inherited neuromuscular disorders selectively affecting the lower motor neuron resulting in progressive proximal manifestation of muscle weakness. The clinical features ranged from weakness of proximal muscles of the lower limb to dysphagia and respiratory dysfunction. Anesthetic management is often difficult in these patients as a result of muscle weakness, respiratory dysfunction, difficult airway management and hypersensitivity to neuromuscular blocking agents. In this case report we describe a child patient with type II Spinal muscular atrophies for left inguinal hernia repair. We decided to use a caudal technique and propofol infusion. We review the available literature and discuss the potential anaesthetic problems in the management of pediatric patients with this degenerative neuromuscular disorder. UR - https://dergipark.org.tr/en/pub/patd/issue//392994 L1 - https://dergipark.org.tr/en/download/article-file/422758 ER -