TY  - JOUR
T1  - Anaesthetic Management of a Patient with Pseudo-TORCH Syndrome
TT  - Anaesthetic Management of a Patient with Pseudo-TORCH Syndrome
AU  - Berk, Derya
AU  - Kuş, Alparslan
AU  - Şahin, Tülay
AU  - Solak, Mine
AU  - Toker, Kamil
PY  - 2013
DA  - March
JF  - Balkan Medical Journal
PB  - Trakya University
WT  - DergiPark
SN  - 2146-3123
SP  - 321
EP  - 322
VL  - 2013
IS  - 3
LA  - en
AB  - Background: Pseudo-TORCH syndrome is a rare, chronic disorder that is characterised by dimorphic features such as microcephaly, intracranial calcification, seizures, mental retardation, hepatosplenomegaly and coagulation disorders.         Case Report: We present the anaesthetic management of a forty day-old boy with Pseudo-TORCH syndrome during magnetic resonance imaging. Microcephaly, growth failure, high palate and bilateral rales in the lungs were detected in pre-anaesthetic physical examination. The peripheral oxygen saturation was 88-89% in room-air and was 95% in a hood with 5 L/min oxygen. We planned general anaesthesia to ensure immobility during magnetic resonance imaging. After standard monitoring, general anaesthesia was induced with 8% sevoflurane in 100% O2. After an adequate depth of anaesthesia was reached, we inserted a supraglottic airway device to avoid intubation without the use of a muscle relaxant.          Conclusion: In patients with Pseudo-TORCH syndrome, the perioperative anaesthetic risk was increased. We believe that using a supraglottic airway device to secure the airway is less invasive than intubation, and can be performed without the need of muscle relaxants.                Turkish         Anahtar Kelimeler:       Psödo-TORCH Sendromu, Anestezi, Supraglottik Hava Yolu Gereci         Arkaplan: Psödo-TORCH sendromu; mikrosefali, intrakraniyal kalsifikasyon, nöbetler, mental retardasyon, hepatosplenomegali ve koagülasyon bozuklukları gibi dimorfik özellikler ile karakterize nadir kronik bir hastalıktır. Manyetik rezonans görüntüleme esnasında Kırk günlük Psödo-TORCH sendromlu erkek bebekteki anestezi yönetimimizi sunmaktayız.          Olgu Sunumu: Anestezi öncesi yapılan fizik muayenesinde mikrosefali, gelişme geriliği, yüksek damak ve akciğerleri dinlemekle bilateral ral tespit edildi. Oda havasında periferik oksijen saturasyonu % 88-89 ve hood eşliğinde 5 lt/dk oksijen ile  % 95 idi. Manyetik rezonans görüntüleme esnasında hareketsizliği sağlamak için genel anestezi planlandı. Standart monitorizasyon sonrası, % 100 oksijen ve % 8 sevofluran ile anestezi indüksiyonu yapıldı. Yeterli anestezi derinliği sağlandıktan sonra, kas gevşetici ajan kullanılmaksızın entübasyondan kaçınmak için supraglottik hava yolu gereci kullanıldı.          Sonuç: Psödo-TORCH sendromlu hastalarda perioperatif anestezi riski artmaktadır. Entübasyona göre daha az invaziv olan supraglottik hava yolu gereçlerinin kas gevşetici ihtiyacı olmaksızın hava yolu güvenliğini sağlayabileceğini düşünüyoruz.
KW  - Pseudo-TORCH syndrome
KW  - anaesthesia
KW  - supraglottic airway device
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UR  - https://dergipark.org.tr/en/pub/bmj/issue//50436
L1  - https://dergipark.org.tr/en/download/article-file/43103
ER  -