Ankara Üniversitesi Tıp Fakültesi Mecmuası

0365-8104 1307-5608

Ankara University

Infant and Child Health Urology

Bebek ve Çocuk Sağlığı Üroloji

Incomplet Prune - Belly Syndrome

iNKOMPLET PRUNE - BELLY SENDROMU

Ekim

Mesiha

ANKARA ÜNİVERSİTESİ, TIP FAKÜLTESİ, DAHİLİ TIP BİLİMLERİ BÖLÜMÜ, ÇOCUK SAĞLIĞI VE HASTALIKLARI ANABİLİM DALI, ÇOCUK NEFROLOJİSİ BİLİM DALI

12 31 1989

42 4 639 646 10 10 1989 12 28 1989

1947

Ankara Üniversitesi Tıp Fakültesi Mecmuası

An eight year old boy was admitted to our clinic because of abdominal distention. He had partial absence of abdominal wall musculature, bilateral hydronephrosis and urethral obstruction. No other abnormalities were identified. Cryptorchidism was not present. Because of this and partial absence of abdominal wall musculature our patient was accepted as incomplet PBS.

Sekiz yaşında bir erkek çocuk karın şişliği nedeniyle kliniğimize yatırıldı. Karın duvarının kaslarında kısmi yokluk, bilateral hidronefroz ve üretra tıkanıklığı vardı. Başka bir anormallik saptanmadı. Kriptorşidizm yoktu. Bu ve karın duvarı kaslarının kısmen yokluğu nedeniyle hastamız eksik PBS olarak kabul edildi.

Syndrome Belly Syndrome Cryptorchidism

hidronefroz üretra tıkanıklığı kriptorşidizm

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2. Duckett JW : The Prune-Belly Syndrome from clinical Pediatric Urology Ed. by Kelalis PP, King LR. WB Saunders Comp Philadelphia-London-Toronto 1976, p : 615-635.

3, Geary DF, MacLusky IB, Churchill BM, McLorie G : A broader spectrum of abnormalities in the Prune-Belly Syndrome. J Urol 135 : 324-326, 1986.

4, Gonzales R, Michael A : Prune-Belly Syndrome from Nelson Textbook of Pediatrics. 13th ed. Ed by Behrman RE, Vaughan VC. WB Saunders Comp. Philadelphia-London Toronto 1987, P. 1157.

5. Meizner I, Bar-Ziv J: Prenatal ultrasonic diagnosis of anterior abdominal wall defects. Eur J Obstet Gynecol Reprod Biol 22 : 217-224, 1986.

6. Moerman P, Fryns JP, Goddeeris P, Lauweryns JM : Pathogenesis of the Prune - Belly Syndrome : A functional urethral obstruction caused by prostatic hypoplasia. Pediatrics 73 : 470-474, 1984.7. Nakayama DK, Harrison MR, Chinn DH, Lorimier AA : The pathogenesis of Prune - Belly. AJDC 138 : 834-836, 1984.

8. Pagon RA, Smith DW, Shepard TH : Urethral obstruction malformation complex : A cause of abdominal muscle deficiency and the «Prune-Belly» J Pediatr 94 : 900-906, 1979.

9. Woodhouse CRJ, Ransley PG, Innes-Williams D : Prune - Belly Syndrome report of 47 cases. Arch Dis Child 57 : 856-859, 1982.