Hirayama Hastalığı (Monomelik Amyotrofi)

Year 2008, Volume: 13 Issue: 4, 274 - 276, 01.08.2008

Tahir Kurtuluş Yoldaş Yıldız Çoruh Hava Dönmez Keklikoğlua Hayriye Gül Polat Bülent Güven

Abstract

Hirayama Hastalığı (HH), genç erkeklerde daha sık görülen benign bir alt motor nöron hastalığıdır. Distal ekstremiteyi tutan ilerleyici güçsüzlük ve sinsi başlangıç ile karekterizedir. Genellikle başlangıcından sonra 5 yıl içinde stabilize olan, benign ve nonprogresif bir hastalık olarak kabul edilir. Biz bu bildiride duysal yakınmanın eşlik etmediği progresif amyotrofi bulguları olan 23 yaşında bir kadın hastayı sunuyoruz.©2008, Fırat Üniversitesi, Tıp Fakültesi

Keywords

Hirayama hastalığı, monomelik amyotrofi, motor nöron hastalığı

Hirayama Disease (Monomelic Amyotrophy)

Abstract

Hirayama Disease (HD) is a benign lower motor neuron disorder in the young with male preponderance. It is characterized by insidious onset and progressive weakness and wasting of a distal extremity . Generally, this disease is considered a 'benign' and non-progressive motor neuron disease, which stabilizes within five years of onset.We describe a 23-year-old famele patient who experienced progressive amyotrophy with no sensorial abnormality.©2008, Firat University, Medical Faculty.

Keywords

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• Kabul Tarihi:22.11.2007