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Tuberosklerozla ilişkili renal anjiomiyolipomun sebep olduğu intraperitoneal kanamayı taklit eden akut retroperitoneal hematom

Year 2012, Volume: 18 Issue: 2, 106 - 108, 01.03.2012

Abstract

Tuberous sclerosis complex (TSC) is known as a neurological and dermatological disorder, but its renal manifestations are frequent and may cause death. We report a patient with TSC who showed bilateral multiple renal angiomyolipomas. Spontaneous retroperitoneal hematoma caused by renal angiomyolipoma that mimicking intraperitoneal hemorrhage was diagnosed in her clinical follow-up. We performed right total nephrectomy for controlling hemorrhage, but she died due to poor respiratory function, in fifteenth day postoperatively.

References

  • 1. Young J, Povey S. The genetic basis of tuberous sclerosis. Mol Med Today 1998;4(7):313-9
  • 2. Van Baal JG, Smits NJ, Keeman JN, Lindhout D, Verhoef S
  • The evolution of renal angiomyolipomas in patients with tuberous sclerosis. J Urol 1994;152(1):35-8
  • 3. Oesterling JE, Fishman EK, Goldman SM, Marshall FF. The management of renal angiomyolipoma. J Urol 1986;135(6):1121-4
  • 4. Harabayashi T, Shinohara N, Katano H, Nonomura K, Shimizu T, Koyanagi T. Management of renal angiomyolipomas associated with tuberous sclerosis complex. J Urol 2004;171(1):102-5
  • 5. Kushwaha R, Dhawan I, Arora R, Gupta K, Dhupia JS
  • Multifocal renal angiomyolipoma presenting as massive intraabdominal hemorrhage. Indian J Pathol Microbiol 2010;53(2):340-1
  • 6. Granata A, Basile A, Figuera M, Mignani R, Fiore CE
  • Spontaneous retroperitoneal hemorrhage due to massive rupture of renal angiomyolipoma treated with nephrectomy: an unusual onset of tuberous sclerosis complex. Clin Nephrol 2009;71(4):441-4
  • 7. Tan BW, Toh KL. Life threatening intraperitoneal hemorrhage with abdominal compartment syndrome: unusual presentation of renal angiomyolipoma. Int J Urol 2010;17(9):820-1
  • 8. Shepherd CW, Gomez MR, Lie JT, Crowson CS. Causes of death in patients with tuberous sclerosis. Mayo Clin Proc 1991;66(8):792-6.

Acute retroperitoneal hematoma mimicking intraperitoneal hemorrhage caused by renal angiomyolipomas associated with tuberous sclerosis

Year 2012, Volume: 18 Issue: 2, 106 - 108, 01.03.2012

Abstract

Tuberoskleroz kompleksi (TSC) nörolojik ve dermatolojik bir hastalık olarak bilinmekteyse de; böbrekte meydana getirdiği değişiklikler nedeniyle sıklıkla karşılaşılabilmekte ve ölüme neden olabilmektedir. Biz bilateral multipl renal anjiomiyolipomu olan tuberosklerozlu bir hastayı sunmak istedik. Renal anjiomiyolipomu olan hastada spontan retroperitoneal hematom meydana geldi ve klinik takiplerinde intraperitoneal kanamayı taklit etmesiyle tanı kondu. Hemorajiyi kontrol etmek için sağ total nefrektomi yapıldı. Ancak hasta post operatif 15. gün zayıf solunum fonksiyonları nedeniyle kaybedildi.

References

  • 1. Young J, Povey S. The genetic basis of tuberous sclerosis. Mol Med Today 1998;4(7):313-9
  • 2. Van Baal JG, Smits NJ, Keeman JN, Lindhout D, Verhoef S
  • The evolution of renal angiomyolipomas in patients with tuberous sclerosis. J Urol 1994;152(1):35-8
  • 3. Oesterling JE, Fishman EK, Goldman SM, Marshall FF. The management of renal angiomyolipoma. J Urol 1986;135(6):1121-4
  • 4. Harabayashi T, Shinohara N, Katano H, Nonomura K, Shimizu T, Koyanagi T. Management of renal angiomyolipomas associated with tuberous sclerosis complex. J Urol 2004;171(1):102-5
  • 5. Kushwaha R, Dhawan I, Arora R, Gupta K, Dhupia JS
  • Multifocal renal angiomyolipoma presenting as massive intraabdominal hemorrhage. Indian J Pathol Microbiol 2010;53(2):340-1
  • 6. Granata A, Basile A, Figuera M, Mignani R, Fiore CE
  • Spontaneous retroperitoneal hemorrhage due to massive rupture of renal angiomyolipoma treated with nephrectomy: an unusual onset of tuberous sclerosis complex. Clin Nephrol 2009;71(4):441-4
  • 7. Tan BW, Toh KL. Life threatening intraperitoneal hemorrhage with abdominal compartment syndrome: unusual presentation of renal angiomyolipoma. Int J Urol 2010;17(9):820-1
  • 8. Shepherd CW, Gomez MR, Lie JT, Crowson CS. Causes of death in patients with tuberous sclerosis. Mayo Clin Proc 1991;66(8):792-6.
There are 11 citations in total.

Details

Primary Language Turkish
Journal Section Articles
Authors

İlker Seçkiner This is me

Aykut Altunkaya This is me

Ömer Bayrak This is me

Bülent Akduman This is me

Aydın Mungan This is me

Publication Date March 1, 2012
Published in Issue Year 2012 Volume: 18 Issue: 2

Cite

APA Seçkiner, İ., Altunkaya, A., Bayrak, Ö., Akduman, B., et al. (2012). Acute retroperitoneal hematoma mimicking intraperitoneal hemorrhage caused by renal angiomyolipomas associated with tuberous sclerosis. Gaziantep Medical Journal, 18(2), 106-108.
AMA Seçkiner İ, Altunkaya A, Bayrak Ö, Akduman B, Mungan A. Acute retroperitoneal hematoma mimicking intraperitoneal hemorrhage caused by renal angiomyolipomas associated with tuberous sclerosis. Gaziantep Medical Journal. March 2012;18(2):106-108.
Chicago Seçkiner, İlker, Aykut Altunkaya, Ömer Bayrak, Bülent Akduman, and Aydın Mungan. “Acute Retroperitoneal Hematoma Mimicking Intraperitoneal Hemorrhage Caused by Renal Angiomyolipomas Associated With Tuberous Sclerosis”. Gaziantep Medical Journal 18, no. 2 (March 2012): 106-8.
EndNote Seçkiner İ, Altunkaya A, Bayrak Ö, Akduman B, Mungan A (March 1, 2012) Acute retroperitoneal hematoma mimicking intraperitoneal hemorrhage caused by renal angiomyolipomas associated with tuberous sclerosis. Gaziantep Medical Journal 18 2 106–108.
IEEE İ. Seçkiner, A. Altunkaya, Ö. Bayrak, B. Akduman, and A. Mungan, “Acute retroperitoneal hematoma mimicking intraperitoneal hemorrhage caused by renal angiomyolipomas associated with tuberous sclerosis”, Gaziantep Medical Journal, vol. 18, no. 2, pp. 106–108, 2012.
ISNAD Seçkiner, İlker et al. “Acute Retroperitoneal Hematoma Mimicking Intraperitoneal Hemorrhage Caused by Renal Angiomyolipomas Associated With Tuberous Sclerosis”. Gaziantep Medical Journal 18/2 (March 2012), 106-108.
JAMA Seçkiner İ, Altunkaya A, Bayrak Ö, Akduman B, Mungan A. Acute retroperitoneal hematoma mimicking intraperitoneal hemorrhage caused by renal angiomyolipomas associated with tuberous sclerosis. Gaziantep Medical Journal. 2012;18:106–108.
MLA Seçkiner, İlker et al. “Acute Retroperitoneal Hematoma Mimicking Intraperitoneal Hemorrhage Caused by Renal Angiomyolipomas Associated With Tuberous Sclerosis”. Gaziantep Medical Journal, vol. 18, no. 2, 2012, pp. 106-8.
Vancouver Seçkiner İ, Altunkaya A, Bayrak Ö, Akduman B, Mungan A. Acute retroperitoneal hematoma mimicking intraperitoneal hemorrhage caused by renal angiomyolipomas associated with tuberous sclerosis. Gaziantep Medical Journal. 2012;18(2):106-8.