Primary plasma cell leukemia: evaluation of a rare disease

Year 2015, Volume: 12 Issue: 2, 300 - 302, 30.08.2015

Fatma Mutlu Sarıguzel Bilal Aygun Çiğdem Karakukcu Vedat Arsav Derya Kocer Ahmet Godekmerdan

Abstract

Plasma cell leukemia (PCL) is a rare and aggressive cancer involving plasma cells. There are two forms of
PCL (with or without multiple myeloma). Although patients with primary and secondary PCL share several
clinical features, important differences exist. We report on a case diagnosed with primary PCL. We analyzed
the clinicopathologic and laboratory features of the disease. The aim of this report is to draw attention to PCL.

Keywords

Plasma cell, primary plasma cell leukemia, multiple myeloma

Primer Plazma Hücreli Lösemi: Nadir Bir Hastalığın Değerlendirilmesi

Abstract

Plazma hücreli lösemi (PHL), plazma hücrelerini içeren agresif ve nadir görülen bir kanserdir. PHL, multle
myelomanın birlikte olduğu ve olmadığı şekilde iki formu (primer, seconder) bulunmaktadır. Primer ve
seconder PHL'li olguların birçok klinik özellikleri benzer olsada önemli farklılıklar bulunmaktadır. Bu olgu
sunumunda primer PHL'li bir hastanın klinik, patolojik ve laboratuar bulguları incelenmiştir. Bu olgu
sunumunun amacı PHL'e dikkat çekmektir. 

Keywords

Plazma hücresi, primer plazma hücreli lösemi, multiple myeloma diskoid

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