CLINICAL EXPERIENCES IN PRIMARY RETROPERITONEAL TUMORS

Year 2018, Volume: 19 Issue: 3, 82 - 85, 23.07.2018

Tamer Sekmenli , İlhan Çiftçi , Doğan Köse , Yavuz Köksal Nevin Sekmenli

https://doi.org/10.18229/kocatepetip.364533

Abstract

Objective: In this study, Selcuk
University Faculty of Medicine between 2011 - 2013 follow-up at the Department
of Pediatric Oncology and Pediatric Surgery clinic was operated by a total of
22 patients with retroperitoneal tumors were evaluated retrospectively .

Patients and Method: Retroperitoneal tumors
were evaluated retrospectively during 2011-2013. The cases treated with primary
retroperitoneal tumor, surgical treatment without other distant organ
metastasis were included in the study. The files of the cases were primary
diagnosis in terms of age, sex, tumor stage at the time of diagnosis, surgical
treatment method, pathological diagnosis and follow-up reviewed
retrospectively.

Results: 9 out of 22 cases (40%) male and
13 (60%) were female. Male mean age of 71 months ( 3-132 ) in the girls 37
months ( 6-204 ) . The histological results, 15 (68%) of neuroblastoma , 4
(18.5%) Wilms, 1 (4.5% ) Embryonal Rhabdomyosarcoma , 1 (4.5% ) Clear cell
sarcoma , 1 (4.5% ) malignant nerve sheath tumors were evaluated . Eight of the
cases (36%) were stage I, 7 (32%) were stage III, 7 (32%) stage IV.

Conclusion: In conclusion, 68% of
our cases were neuroblastoma and 64% of the patients were stage III and stage
IV at the time of diagnosis. Retroperitoneal tumors are generally diagnosed in
advanced stages. We think that this is due to the anatomical localizations and
the silent as far as the clinically advanced stage. 

Keywords

retroperitoneal tumor, neuroblastoma, pediatric

PRİMER RETROPERİTONEAL TÜMÖRLERDE KLİNİK DENEYİMLERİMİZ

Abstract

Amaç: Bu çalışmada Selçuk
Üniversitesi Tıp Fakültesi 2011-2013 tarihleri arasında Çocuk Onkoloji Anabilim
Dalı’nda takipli ve Çocuk Cerrahisi Kliniğince opere edilen toplam 22
retroperitoneal tümörlü hastaların kayıtları retrospektif olarak
değerlendirildi.

Olgular ve Yöntem: Retroperitoneal
tümör nedeniyle 2011-2013 arasında cerrahi girişim yapılan olgular geriye dönük
olarak incelendi. Primer retroperitoneal tümörü kontrol altına alınan, başka
uzak organ metastazı olmayan cerrahi tedavi uygulanan olgular çalışmaya dahil
edildi. Yaş, cinsiyet, primer tanı anında tümör evresi, cerrahi tedavi yöntemi,
patolojik tanı ve takip açısından olguların dosyaları retrospektif olarak
değerlendirildi.

Bulgular: Olgularımızın 9’u (%40)
erkek, 13’ü (%60) kızdı.  Ortalama yaş erkeklerde
71 ay (3-132), kızlarda 37 ay (6-204) idi. Histopatolojik olarak olguların 15 (%68)’i
nöroblastom,  4’ü (%18.5) wilms tümörü,
1’i (%4.5) embriyonal rabdomyosarkom, 1’i (%4.5) berrak hücreli sarkom, 1’i (%4.5)
malign sinir kılıfı tümörü olarak değerlendirildi. Tanı anında olguların 8’i (%36)
evre I, 7’si (%32) Evre III, 7’si (%32) evre IV safhasındaydı.

Sonuç: Olgularımızın %68’i nöroblastom
olup, tanı anında hastaların %64’ü evre III ve evre IV idi. Anatomik
lokalizasyonları nedeniyle ileri evrelere kadar sessiz tümörler olan retroperitoneal
tümörlerin çoğu nöroblastomdur ve genellikle ileri evrelerde tanı alırlar. 

Keywords

retroperitoneal tümör, nöroblastoma, pediatrik

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