LAPAROSCOPIC APPENDECTOMY IN DYSTROPHIC EPIDERMOLYSIS BULLOSA: ADVANTAGES OF MINIMALLY INVASIVE PROCEDURE
Abstract
Dystrophic epidermolysis bullosa (DEB) is an
epidermolysis bullosa (EB) type that bulla formation
develops on the dermal surface of the
dermoepidermal component due to splitting in
the basal lamina. In these patients, opening of
mechanical blisters caused by trauma can lead
to infection.
In cases with DEB, surgical intervention, especially
in the case of abdominal surgery, requires
careful attention to prevent infection of the
blisters caused by incision and surgery. Here we
present a 16-year-old male having DEB who had
undergone laparoscopic appendectomy with a
diagnosis of perforated appendicitis. Preoperative
and postoperative interventions have to be
planned to cause minimal trauma and infection
to the skin and preference for a less invasive laparoscopic
approach is the approach
Keywords
Epidermolysis bullosa Dystrophic epidermolysis bullosa Perforated appendicitis Laparoscopic appendectomy
References
- 1. Karaduman A. Kalıtsal büllü hastalıklar. Türkderm 2011;45(2):81-6.
- 2. Sousa MC, Paula CD, Tauil PL, Costa IM. Correlation between nutritional, hematological and infectious characteristics and classification of the type ofepidermolysisbullosa of patients assisted at the Dermatology Clinic of the Hospital Universitário de Brasília. An Bras Dermatol 2015;90(6):922-4.
- 3. Elluru RG, Contreras JM, Albert DM. Management of manifestations of epidermolysis bullosa. Curr Opin Otolaryngol Head Neck Surg 2013;21(6):588-93.
- 4. Denyer J, Gibson E. Use of fibre dressings in children with severe epidermolysis bullosa. Br J Nurs 2015;24(6):38-40.
- 5. Jesus LED, Rangel M, Mauro-Filho RS. Urological surgery in epidermolysis bullosa: tactical planning for surgery and anesthesia. Int Braz J Urol2014;40(5):702-7.
- 6. Bıçakçı Ü, Tander B, Çakmak Çelik F, Arıtürk E, Rızalar R. Pilor atrezisi ve epidermolizis bülloza birlikteliği: İki olgu sunumu ve literatür derlemesi. Ulus Travma Acil Cerrahi Derg 2012;18(3):271-3.
- 7. Ksia A, Zitouni H, Zrig A, Laamiri R, Chioukh F, Ayari E, Sahnoun L, Maazoun K, Krichene I, Mekki M, Belghith M, Nouri A. Pyloric atresia: A report of ten patients. Afr J Pediatr Surg. 2013;10(2):192-4.
- 8. Stehr W, Farrell MK, Lucky AW, Johnson ND, Racadio JM, Azizkhan RG. Nonendoscopic percutaneous gastrostomy placement in children with recessive dystrophic epidermolysis bullosa. Pediatr Surg Int 2008;24(3):349-54.
- 9. Gollu G, Ergun E, Ates U, Can OS, Dindar H. Baloon dilatation in eusophageal strictures in epidermolysis bullosa and the role of anesthesia. Dis Esophagus 2017;30(3):1-6.
- 10. Elton C, Marshall REK, Hibbert J, Cameron R, Mason RC. Pharyngogastric colonic interposition for total oesophageal acclusion in epidermolysis bullosa. Dis Esophagus
Abstract
Keywords
Epidermolizis bülloza Distrosfik epidermolizis bülloza Perfore apendisit Laparoskopik appendektomi
References
- 1. Karaduman A. Kalıtsal büllü hastalıklar. Türkderm 2011;45(2):81-6.
- 2. Sousa MC, Paula CD, Tauil PL, Costa IM. Correlation between nutritional, hematological and infectious characteristics and classification of the type ofepidermolysisbullosa of patients assisted at the Dermatology Clinic of the Hospital Universitário de Brasília. An Bras Dermatol 2015;90(6):922-4.
- 3. Elluru RG, Contreras JM, Albert DM. Management of manifestations of epidermolysis bullosa. Curr Opin Otolaryngol Head Neck Surg 2013;21(6):588-93.
- 4. Denyer J, Gibson E. Use of fibre dressings in children with severe epidermolysis bullosa. Br J Nurs 2015;24(6):38-40.
- 5. Jesus LED, Rangel M, Mauro-Filho RS. Urological surgery in epidermolysis bullosa: tactical planning for surgery and anesthesia. Int Braz J Urol2014;40(5):702-7.
- 6. Bıçakçı Ü, Tander B, Çakmak Çelik F, Arıtürk E, Rızalar R. Pilor atrezisi ve epidermolizis bülloza birlikteliği: İki olgu sunumu ve literatür derlemesi. Ulus Travma Acil Cerrahi Derg 2012;18(3):271-3.
- 7. Ksia A, Zitouni H, Zrig A, Laamiri R, Chioukh F, Ayari E, Sahnoun L, Maazoun K, Krichene I, Mekki M, Belghith M, Nouri A. Pyloric atresia: A report of ten patients. Afr J Pediatr Surg. 2013;10(2):192-4.
- 8. Stehr W, Farrell MK, Lucky AW, Johnson ND, Racadio JM, Azizkhan RG. Nonendoscopic percutaneous gastrostomy placement in children with recessive dystrophic epidermolysis bullosa. Pediatr Surg Int 2008;24(3):349-54.
- 9. Gollu G, Ergun E, Ates U, Can OS, Dindar H. Baloon dilatation in eusophageal strictures in epidermolysis bullosa and the role of anesthesia. Dis Esophagus 2017;30(3):1-6.
- 10. Elton C, Marshall REK, Hibbert J, Cameron R, Mason RC. Pharyngogastric colonic interposition for total oesophageal acclusion in epidermolysis bullosa. Dis Esophagus
Details
| Primary Language | Turkish |
|---|---|
| Journal Section | Case Report |
| Authors | |
| Publication Date | October 26, 2018 |
| Acceptance Date | September 12, 2017 |
| Published in Issue | Year 2018 Volume: 19 Issue: 4 |
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