Rare Calcified Pseudoneoplasm of Neuraxis Presenting with Seizure in Children (CAPNON)

Year 2022, Volume: 10 Issue: 3, 131 - 133, 31.12.2022

Kübra Taşar , Abdullah Canbal , Burcu Çalışkan , Saliha Yavuz Eravcı Cengiz Kadıyoran , Mehmet Fatih Erdi , Ahmet Güven

https://doi.org/10.21765/pprjournal.1223145

Abstract

Calcified pseudoneoplasms of neuraxis (CAPNON) are nonneoplastic and rare lesions of the central nervous system. Its etiology is unclear and its surgical removal is usually curative. Its radiographic features were defined by prominent calcifications seen on computed tomography (CT) and hypointensity on T1- and T2-weighted images with variable enhancement on magnetic resonance (MR) imaging. CANON, which is not common in adults, is very rare in children. The majority of reported CAPNON tumors are intracranial, although the spinal cord may also be found. It may be asymptomatic or present with headaches, seizures and focal neurological deficits when symptomatic. We present a case of a 12-year-old boy who presented with focal seizure episodes accompanied by variable consciousness and was diagnosed as CAPNON, which was rarely reported in the literature, and was followed up without surgery.

Keywords

Calcified pseudoneoplasms of neuraxis (CAPNON), child, brain tumor, seizure

Çocuklarda Nöbet ile Prezente Olan Nadir Görülen Nöraksisin Kalsifiye Psödoneoplazmı (CAPNON)

Abstract

Nöraksisin kalsifiye psödoneoplazmaları (CAPNON), santral sinir sisteminin nonneoplastik ve nadir görülen lezyonlarıdır. Etiyolojisi belirsizdir ve cerrahi olarak çıkarılması genellikle küratiftir. Radyografik özellikleri, bilgisayarlı beyin tomografide belirgin kalsifikasyonlar ve manyetik rezonans (MR) görüntülemede değişken kontrastlanma gösteren, T1 ve T2 ağırlıklı görüntülerde hipointensite görülmesiyle tanımlanmıştır. Erişkinlerde de sık rastlanmayan CAPNON, çocuklarda ise çok nadir görülmektedir. Bildirilen CAPNON tümörlerinin büyük çoğunluğu intrakraniyal olmakla birlikte, spinal kord da bulunabilir. Asemptomatik olabildiği gibi semptom gösterdiğinde de baş ağrıları, nöbet ve fokal nörolojik defisitler ile presente olabilir. Literatürde çok nadir bildirilen, değişken bilincin eşlik ettiği fokal nöbet epizodları ile başvuran ve CAPNON tanısı alan opere olmadan takip edilen 12 yaşında çocuk olguyu sunuyoruz.

Keywords

Nöraksisin kalsifiye psödoneoplazmaları (CAPNON), çocuk, beyin tümör, seizure, Calcified pseudoneoplasms of neuraxis (CAPNON), child, brain tumor, seizure

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