tjfmpc Turkish Journal of Family Medicine and Primary Care 1307-2048 Aile Hekimliği Akademisi Derneği 10.21763/tjfmpc.610837 ​Internal Diseases İç Hastalıkları A Three-Stage Assessment of a Case of Polycystic Liver Disease, Based on the Principles of Family Medicine Kini Sanjay Dept. of Community Medicine, KS Hegde Medical Academy, Deralakatte, Mangalore 575018, India. 09 20 2019 13 3 396 401 03 18 2019 05 14 2019 Copyright © 2007, Turkish Journal of Family Medicine and Primary Care 2007 Turkish Journal of Family Medicine and Primary Care

Background:Nowadays there is anincreasing trend of diagnosis of hepatic cysts due to widespread use ofultrasound examination. However, the vast majority of these cysts are benignand have an indolent course during the lifespan of the patient. Secondary toenlarging cyst size and hepatomegaly, the minority of patients develop clinicalsymptoms. Aim: Applyingthe consultation model of three-stage assessment (ie, Clinical, individual andcontextual assessment) based on the principles of family medicine, in the evaluation of a patientwith polycystic liver disease. Method: We present a case of polycystic liver disease, with clinicalmanifestations like palpable liver, shifting dullness, elevated bilirubinlevels and evaluated using three-stage-assessment model. Result: Patient had a positive attitude towards herhealth, but suffered neglect from family members. Conclusion: Positive attitude towards health anddisease, emotional support of family members, regular follow-up with theconsulting physician and genetic counseling of couples who are planning toconceive and have a family history of polycystic liver disease are some of thekey facts emphasized when we applied the three-stage-assessment model in thisparticular case.  Giriş: Günümüzde, ultrason incelemesinin yaygınkullanımı nedeniyle hepatik kistlerin teşhisinde artış eğilimi vardır. Bununlabirlikte, bu kistlerin büyük çoğunluğu iyi huyludur ve hastanın yaşamı boyuncayavaş ilerleyen bir seyre sahiptir. Büyüyen kist büyüklüğü vehepatomegaliye  ikincil olarak, az sayıdahastada klinik semptomlar geliştirir. Amaç:Polikistik karaciğer hastalığı olan bir hastanın değerlendirilmesinde AileHekimliği İlkelerini temel alan üç aşamalı değerlendirme modelinin (örneğin;klinik, bireysel ve bağlamsal değerlendirme) uygulanması. Yöntem: Klinik olarak palpe edilebilir karaciğer, yer değiştirenmatite, artan bilirubin düzeyleri ile sunduğumuz polikistik karaciğer olgusu,üç aşamalı değerlendirme modeli kullanılarak incelendi. Bulgular: Hastanınsağlığı konusunda olumlu bir tutumu vardı, fakat aile üyeleri tarafından ihmalediliyordu. Sonuç: Üç aşamalıdeğerlendirme modelini uyguladığımız bu özel olguda; sağlık ve hastalığa karşıolumlu tutum, aile üyelerinin duygusal desteği, danışılan hekimin düzenliizlemi ve çocuk sahibi olmayı planlayan ve ailede polikistik karaciğerhastalığı öyküsü olan çiftlerin genetik danışmanlığı kilit noktalar olarakvurgulanmıştır.

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