VACTERL SYNDROME: DIFFERENT DENTAL FINDINGS

Year 2021, Volume: 4 Issue: 1, 7 - 10, 07.04.2021

Tuğba Yiğit Zuhal Kırzıoğlu Rüya Alpar

Abstract

VACTERL syndrome is a congenital malformation that effects multisystem. The characteristic symptoms of this syndrome are vertebral anomalies (V), anal atresia (A), cardiac defects (C), tracheoesophageal fistula together with esophageal atresia (TE), radial dysplasia, renal anomalies (R), and limb defects (L). The prevalence of VACTERL syndrome is 1/10,000-1/40,000. Clinical diagnosis can be made with at least three out of the symptoms. Oral manifestation of VACTERL syndrome has not been reported in the literature. Oral findings are the most noticeable point of his syndrome. So, we aimed to draw attention to oral findings in the syndrome in this study. This is the first case report that investigated oral/dental findings which accompany supernumerary teeth and early tooth eruption as well as medical findings.

Keywords

Supernumerary teeth, oral hygiene, VACTERL syndrome

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