TY - JOUR T1 - İKİ VAKA NEDENİYLE TROMBOTİK TROMBOSİTOPENİK PURPURA AU - Ersoy, Uğur AU - Akdoğan, M. Fatih AU - Palit, Fatih AU - Şavlı, Haluk AU - Mağın, Hasan AU - Gücün, Murat AU - All., At PY - 2011 DA - November JF - Journal of Istanbul Faculty of Medicine JO - İst Tıp Fak Derg PB - İstanbul Üniversitesi WT - DergiPark SN - 1305-6441 SP - 124 EP - 126 VL - 71 IS - 4 LA - tr AB - Trombotik Trombositopenik Purpura (TTP) ; Ateş, akut böbrek yetmezliği, nörolojik bozukluklar, trombositopeni ve mikroanjiopatik hemolitik anemi ile seyreden bir sendromdur. Nadir görülen bu hastalık (4-11/1.000.000), klinik olarak dissemine intravasküler koagulasyon (DİK), hemolitik üremik sendrom (HÜS) ve Evans sendromu gibi anemi yapan diğer nedenlerle karışabilir. İki vaka nedeniyle, TTP güncel literatür ışığında tekrar gözden geçirilmiştir. KW - Trombositopeni KW - Purpura KW - Plazmaferez CR - Allford SL,Hunt BJ, Rose P, Machine S. Guidelines on the diag- nosis and management of the thrombotic microangiopathic ha- emolytic anaemias. Br J Haematol 2003;120:556-573. CR - Carmichae DS , Medley DRK .Heparin in thrombotic microan- giopathy Lancet 1966;1:1421-1424. CR - Current concepts in thrombotic thrombocytopenic purpura. Annu Rev Med 2006; 57: 419-436). CR - Del Zoppo, G.J.: Antiplatelet theraphy in thrombotic throm- bocytopenic purpura. Semin Hematology 1987; 24:32. CR - Elliot MA, Nichols, WL.Thorombotic trombositopenic purpura and hemolitic uremic syndrome.Mayo Clin Proc 2001;76:1154- 1162. CR - Feldman JD , Mardiney MR ,Unanue ER ,Cutting H .The vascu- lar pathology of thrombotic thrombocytopenic purpura .An im- munohistochemical and ultra structural study. Lab Invest 1966;15:927-946. CR - GA Rock. KH Shumak. NA Buskard.VS Blanchette.JG Kel- ton.RC Nair and RA Spasoff comparison of plasma exchange with plasma infusion in the treatment of thrombotic thrombocy- topenic purpura canadian Apheresis study group N Eng J Med 1991;325:393-397. CR - James N.George How I treat patients with thrombotic throm- bocytopenic purpura- hmolytic uremic syndrome. Blood 2000 ;96:1223-1229. CR - George JN,Gilcher RO,Smith JW , Chandler L, Duvall D.Thrombotic Thrombocytopenic Purpura – Hemolytic Uremic Syndrome : diagnosis nand manangement .J Clin Apheresis 1998;13:120-125. CR - Havens ,P.L.,O’Rouke P.P.,Hahn,J.,Higgins,J., Walker,A.M.:La- boratory and clinical varables to predict outcome in hemolytic- üremic syndrome AJDC 1988;142:961. CR - James N. George, Thorombotic trombositopenic purpura N Engl J Med 2006;354:1927-3195. CR - Kennedy SS, Zacharsky LR,Beck JR.Thrombotic thrombosito- penic purpura :analysis of 48 unselected cases. Semin Thromb Hemost 1980;6:341-349. CR - Kutell MA ,Alfrey CP ,Hetting RA.TTP treatment N Engl J Med 1971;285:971-972. CR - Melnyk, A.M.S.,Solez K., Kjellstrand, C.M.:Hemolytic uremic syndrome in adults. Arch Intern Med 1995;155:2077. CR - Miller,J.M., Pastorek ,JG.:Thrombotic thrombocytopenic purpu- ra and hemolytic üremic syndrome in pregnancy.Clin Obstet Gynecol 1991;34:41. CR - Neame PB.Immunologic and other factors in thrombotic throm- bocytopenic purpura (TTP). semin Thromb Hemost 1980;6:416- 429. CR - Ponticelli,C.,Rivolta ,E.,Imbasciati ,E., Rossi,E., Mannuc- ci,P.M.:Hemolytic üremic syndrome. Arch Intern Med 1980; 140:335. CR - Rock ,G.A.,Shumak,K.H.,Buskard ,N.A.: Comparision of plasma Exchange with plasma infusion the treatment of TTP N Eng J Med 1991;325:326. CR - Rock G ,Porta C , Bobbio-Pallavicini E.Thrombotic thrombocy- topenic purpura treatment in year 2000.Haematologica 2000; 85:410-419. CR - Sadler JE,Moake JL. Recent advances in thrombotic trombocyto- penic purpura American Society of Hematology, 2004; 407-423. CR - Terrell DR, Williams LA, Vesely SK,Lammle B, Hovinga JA, George JN,The incidence of thrombotic thrombocytopenic pur- pura-hemolytic uremic syndrome: all patients, idiopathic patients, and patients with severe ADAMTS-13 deficiency. J Thromb Ha- emost 2005; 3:1432-1436. CR - Weinstein ,L.: Syndrome of hemolysis, elevated liver enzymes and low platelet count : A severe consequence of hypertension in pregnancy. Am J Obstet Gynecol 1982; 142:159. UR - https://dergipark.org.tr/tr/pub/iuitfd/issue//115948 L1 - https://dergipark.org.tr/tr/download/article-file/98358 ER -