TY - JOUR T1 - Demographic, Clinical and Echocardiographic Characteristics of Children with Chest Wall Deformities Göğüs Duvarı Deformitesi Olan Çocukların Demografik, Klinik ve Ekokardiyografik Özellikleri TT - Göğüs Duvarı Deformitesi Olan Çocukların Demografik, Klinik ve Ekokardiyografik Özellikleri AU - Aslan, Eyüp AU - Sert, Ahmet AU - Sap, Fatih AU - Aypar, Ebru AU - Odabaş, Dursun PY - 2017 DA - August JF - Güncel Pediatri PB - Galenos Yayınevi WT - DergiPark SN - 1304-9054 SP - 34 EP - 37 VL - 15 IS - 2 LA - en AB - INTRODUCTION: To determine thedemographic, clinical and echocardiographic characteristics of children withchest wall deformities.METHODS: The patients diagnosed with chest wall deformities were investigatedretrospectively in the pediatric cardiology unit over a period of three years.The study enrolled 205 children under the age of 18 years diagnosed with chestwall deformities. RESULTS: The mean age of the patients was 7.6 ± 4.5 years with a median of 8years. One hundred and sixty four (80 %) patients with chest wall deformitieswere found to have normal echocardiography results. Incidentalechocardiographic diagnoses included 10 (4.87%) atrial septal defects, 8(3.90%) mitral valve prolapses, 7 (3.41%) mild mitral regurgitations, 5 (2.44%)bicuspid aortic valve without aortic valve stenoses, 4 (1.95%) ventricularseptal defects, 2 (0.98%) mild aortic regurgitations, 2 (0.98%) dextrocardia, 2(0.98%) coarctations of the aorta, and 1(0.49%) complex cardiac defect (pulmonary atresia and VSD). Compression in theright heart was evaluated by echocardiography in 15 patients (7.3%).DISCUSSION AND CONCLUSION: Because chest wall deformities are associated withcongenital heart defects in children and may cause compression in the rightheart, evaluation by echocardiography can ensure an optimal management of thedefects. KW - Child KW - echocardiography KW - chest wall deformity KW - Çocuk KW - ekokardiyografi KW - göğüs duvarı deformitesi N2 - GİRİŞ ve AMAÇ: Göğüs duvarı deformitesiolan çocukların demografik, klinik ve ekokardiyografik özelliklerinindeğerlendirilmesi amaçlandı.YÖNTEM ve GEREÇLER: Çocuk kardiyoloji ünitesinde üç yıl süreyle göğüs duvarıdeformitesi tanısı alan hastalar retrospektif olarak değerlendirildi.BULGULAR: Ortanca yaşı 8 olan hastaların ortalama yaşı 7.6 ± 4.5 idi. Göğüsduvarı deformitesi olan yüz altmış dört (% 80) hastanın ekokardiyografikdeğerlendirmesi normaldi. Ekokardiyografik tanıları 10 (% 4.87) atriyal septaldefekt, 8 (% 3.90) mitral kapak prolapsusu, 7 (% 3.41) hafif mitralyetersizliği, 5 (% 2.44) darlık olmayan biküspit aort kapağı, 4 (% 1.95)ventriküler septal defekt, 2 (% 0.98) hafif aort kapak yetersizliği, 2 (% 0.98)dekstrokardi, 2 (% 0.98) aort koarktasyonu ve 1 (% 0.49) kompleks kalp defekti(pulmoner atrezi ve ventriküler septal defekt) idi. Ekokardiyografi iledeğerlendirilen sağ kalbe bası bulgusu 15 (% 7.3) hastada saptandı.TARTIŞMA ve SONUÇ: Göğüs duvarı deformitelerinin doğuştan kalp hastalıkları ileilişkili olması ve kalbe bası bulgusu oluşturabilmeleri sebebiyleekokardiyografi ile değerlendirilmesi defektlerin en uygun şekildeyönetilmesini sağlayacaktır.ABSTRACTINTRODUCTION: To determine thedemographic, clinical and echocardiographic characteristics of children withchest wall deformities.METHODS: The patients diagnosed with chest wall deformities were investigatedretrospectively in the pediatric cardiology unit over a period of three years.The study enrolled 205 children under the age of 18 years diagnosed with chestwall deformities. RESULTS: The mean age of the patients was 7.6 ± 4.5 years with a median of 8years. One hundred and sixty four (80 %) patients with chest wall deformitieswere found to have normal echocardiography results. Incidentalechocardiographic diagnoses included 10 (4.87%) atrial septal defects, 8(3.90%) mitral valve prolapses, 7 (3.41%) mild mitral regurgitations, 5 (2.44%)bicuspid aortic valve without aortic valve stenoses, 4 (1.95%) ventricularseptal defects, 2 (0.98%) mild aortic regurgitations, 2 (0.98%) dextrocardia, 2(0.98%) coarctations of the aorta, and 1(0.49%) complex cardiac defect (pulmonary atresia and VSD). Compression in theright heart was evaluated by echocardiography in 15 patients (7.3%).DISCUSSION AND CONCLUSION: Because chest wall deformities are associated withcongenital heart defects in children and may cause compression in the rightheart, evaluation by echocardiography can ensure an optimal management of thedefects. CR - 1. Fokin AA, Steuerwald NM, Ahrens WA, Allen KE. Anatomical, histologic, and genetic characteristics of congenital chest wall deformities. Semin Thorac Cardiovasc Surg 2009;21:44-57. CR - 2. Brochhausena C, Salmai T, Müllera FKP, Schmitta VH, Coerdta W, Wihlmc JM, Schierb F, Kirkpatricka CJ. Pectus excavatum: history, hypotheses and treatment options. Interactive CardioVascular and Thoracic Surgery 2012;14: 801–6. CR - 3. Park JM, Varma SK. Pectus excavatum in children : Diagnostic significance for mitral valve prolapse. The Indian Journal of Pediatrics 1990;57 219-22. 4. Tang M, Nielsen HH, Lesbo M, Frøkiær J, Maagaard M, Pilegaard HK, Hjortdal VE. Improved cardiopulmonary exercise function after modified Nuss operation for pectus excavatum. Eur J Cardiothorac Surg 2012;41:1063-7. CR - 5. Desmarais TJ, Keller MS. Pectus carinatum. Curr Opin Pediatr 2013;25:375-81. CR - 6. Shamberger RC, Welch KJ, Castaneda AR, Keane JF, Fyler DC. Anterior chest wall deformities and congenital heart disease. J Thorac Cardiovasc Surg 1988:96(3):427-32. CR - 7. Simsek Z, Gunay E, Aksakal E, Kutucularoglu MG, Guneren G. İzole pektus ekskavatumlu genç erişkin hastaların kardiyopulmoner bulgularının değerlendirilmesi. Anadolu Kardiyol Derg 2011;1:77-8. CR - 8. Akcali Y, Ceyran H, Hasdiraz L. Chest wall deformities. Acta Chir Hung 1999; 38:1-3. CR - 9. Esme H, Bukulmez A, Dogru O, Solak O. Afyon ili ilköğretim okulu çocuklarında gögüs duvarı deformitelerinin prevalansı. Turkish J Thorac Cardiovasc Surg 2006;14:34-7. CR - 10. Randhawa AK, Mishra C, Gogineni SB, Shetty S. Marfan syndrome: report of two cases with review of literature. Niger J Clin Pract 2012;15:364-8. CR - 11. Kikuchi S, Ingu A, Ito M. Simultaneous repair of pectus excavatum and tetralogy of fallot: report of a case. Ann Thorac Cardiovasc Surg 2005;11:320-3. CR - 12. Coln E, Carrasco J, Coln D. Demonstrating relief of cardiac compression with the Nuss minimally invasive repair for pectus excavatum. J Pediatr Surg 2006;41:683-6. CR - 13. Guntheroth WG, Spiers PS. Cardiac function before and after surgery for pectus excavatum. Am J Cardiol 2007;12:1762-4. UR - https://dergipark.org.tr/tr/pub/pediatri/issue//331288 L1 - https://dergipark.org.tr/tr/download/article-file/333432 ER -