TY - JOUR T1 - Megameatus intact prepuce and associated anomalies AU - Ekberli, Günay AU - Ateş, Ufuk AU - Sözduyar, Sümeyye AU - Gurbanov, Anar AU - Göllü, Gülnur AU - Koloğlu, Meltem AU - Yağmurlu, Aydın AU - Dindar, Hüseyin AU - Çakmak, Ahmet PY - 2020 DA - December Y2 - 2020 DO - 10.16899/jcm.705034 JF - Journal of Contemporary Medicine JO - J Contemp Med PB - Rabia YILMAZ WT - DergiPark SN - 2667-7180 SP - 542 EP - 545 VL - 10 IS - 4 LA - en AB - Objective: Megameatus intact prepuce is described as subset of megalourethra or distal hypospadias by several authors. Despite suggested different operative techniques, some authors prefer not to operate this variant of penile anomaly. We aimed to evaluate 31 patients operated due to megameatus intact prepuce and associated anomalies .Material and methods: Thirtyone patients operated between 2008-2018 for MIP were evaluated retrospectively. All data were collected from hospital records. Patient age, application reasons, raphe anomalies, associated genitourinary and extragenitourinary pathologies, operative techniques, and postoperative complications were analyzed. Results: Mean age was 50 months (8-128 months). Ten of the patients had raphe anomalies. Genital raphe hyperpigmentation was seen in 1 patient, raphe deviation and bifurcated raphe was seen in6 and 3 patients respectively. Genitourinary anomalies were detected in 7 patients, bilateral undescended testes in 1 patient, penile chordee in 2 patients, ureteropelvic junction obstruction in 2 patients, penoscrotal web in 1 patient, nocturnal enuresis in one patient. Tubularized incised plate urethroplasty (TIPU) (n=5), tubularized urethral plate urethroplasty (TUPU)(n=16) and meatoplasty (n=10) were the operative techniques.Conclusion: . Co-occuring raphe anomalies should arise awareness of MIP among the clinicians who are engaged with the children’s medical conditions and also the possible anomalies especially in the societies which circumcision is not traditionally required. Further studies with large number series needed for better understanding of this pathology. KW - Megameatus intact prepuce KW - KW - associated anomalies CR - 1-Juskiewenski S. Vaysse P, Moscovici J. Treatment of anterior hypospadias. (Balanoplasty) (Article in French). J Urol. 1983;89:153-156 CR - 2-Duckett JW, Keating MA. Technical challenge of the megameatus intact prepuce hypospadias variant: the pyramid procedure. J Urol. 1989;141:1407-1409 CR - 3-Peretz D, Westreich M. Pseudo-iatrogenic hypospadias: the megameatus intact-prepuce hypospadias variant. Plast Reconstr Surg. 2003;111:1182-1185 CR - 4- Fahmy M, Shenaway A, Altramsy A, Al Samahy O, Yehya A, Othman D. 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BJU Int 2004;94:1188–1195 UR - https://doi.org/10.16899/jcm.705034 L1 - https://dergipark.org.tr/tr/download/article-file/1009736 ER -