The retrocaval ureter is a rare congenital anomaly in which the right ureter passes behind the vena cava inferior, leading to varying degrees of ureteral compression. Its incidence is 1/1500. It has been accepted that an embryological abnormal development of inferior vena cava has a role, on its etiology. In this case report the clinical diagnosis and treatment of symtomatic retrocaval ureter was assessed in a 28 years old male patient.