6 years old female patient referred for a mass over the right upper eyelid and ptosis, also revealed co-existing bilateral Lisch nodules and cafe-au-laid spots . MRI graphics revealed plexiform neurofibroma extending from right upper eyelid to cavernous sinus and trigeminal nerve. We concluded that one should make the differential diagnosis especially patients presented, during first decade of life, with mass over the upper eyelid and ptosis