A Case of Sarcoidosis with Atypical Presentation

Yıl 2024, Cilt: 8 Sayı: 2, 257 - 261, 27.08.2024

Duygu Acer , Mehmet Veysel Coşkun , Selma Karaahmetoğlu , Ali Can Kurtipek

https://doi.org/10.46332/aemj.1381010

Öz

Sarcoidosis is a multisystemic disease characterized by non-caseating granulomas of unknown etiology. While pulmonary manifestations are present in 90% of cases, extrapulmonary sarcoidosis cases are rare and diagnosis is often challenging due to atypical clinical course. Here, we aim to present a case of extrapulmonary sarcoidosis diagnosed after excluding Macrophage Activation Syndrome and lymphoma during clinical follow-up.

Anahtar Kelimeler

lymphoma, macrophage activation syndrome, sarcoidosis

Atipik Prezentasyon Gösteren Sarkoidoz Olgusu

Öz

Sarkoidoz, nonkazeifiye granülomlarla karakterize, etiyolojisi bilinmeyen multisistemik bir hastalıktır. Olguların %90'ında akciğer bulguları mevcut olmakla birlikte, ekstrapulmoner sarkoidoz olguları oldukça nadirdir ve atipik klinik seyir nedeniyle tanı koymak genellikle zordur. Burada klinik takibinde Makrofaj aktivasyonu sendromu ve lenfoma ekarte edildikten sonra tanısı konulan bir ekstrapulmoner sarkoidoz olgusunu sunmayı amaçladık.

Anahtar Kelimeler

lenfoma, makrofaj aktivasyonu sendromu, sarkoidoz

Kaynakça

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