Rapunzel Syndrome Causing Gastric Outlet Obstruction in A 12-Year-Old Girl: Report of A Case and Review of the Literature

Bilge Gördü; Tutku Soyer

doi:10.4274/atfm.galenos.2023.03064

EN TR

Rapunzel Syndrome Causing Gastric Outlet Obstruction in A 12-Year-Old Girl: Report of A Case and Review of the Literature

Abstract

Rapunzel syndrome (RS) is a rare condition presenting with hair accumulation in the stomach that extends to small intestine. It may cause gastric outlet and intestinal obstruction. The most common clinical signs are abdominal pain, palpable mobile mass and vomiting. A 12-year-old girl with a history of trichotillomania, trichophagia, attention deficit and hyperactivity disorder presented with gastric outlet obstruction. A bezoar completely filling the stomach and reaching to third part of the duodenum was detected in abdominal ultrasound. Removal of the trichobezoar via gastrotomy was the treatment of choice. Herein we report a 12-year-old girl with RS to discuss the clinical features and treatment options in this rare presentation. Key Words: Bezoar, trichobezoar, Rapunzel Syndrome, child

Keywords

Bezoar, trichobezoar, Rapunzel Syndrome, child

Ethical Statement

Informed consent was obtained from the patient’s family.

12 Yaşındaki Bir Kız Çocukta Mide Çıkım Tıkanıklığına Neden Olan Rapunzel Sendromu: Olgu Sunumu ve Literatürün Gözden Geçirilmesi

Abstract

Rapunzel sendromu (RS) midede biriken saçların ince barsakta obstrüksiyona neden olabilecek şekilde uzandığı nadir bir durumdur. Mide çıkımında ve barsakta tıkanıklığına neden olabilir. En sık görülen klinik belirtiler karın ağrısı, ele gelen mobil kitle ve kusmadır. Trikotilomani, trikofaji, dikkat eksikliği ve hiperaktivite bozukluğu öyküsü olan 12 yaşında kız hasta, mide çıkım tıkanıklığı nedeniyle başvurdu. Batın ultrasonunda mideyi tamamen dolduran ve duodenumun üçüncü kısmına uzanan bezoar tespit edildi. Trikobezoarın gastrotomi yoluyla çıkarılması tercih edildi. Burada, bu nadir görülen tablonun klinik özelliklerini ve tedavi seçeneklerini tartışmak amacıyla 12 yaşında RS’li bir kız çocuğunu sunuyoruz. Anahtar Kelimeler: Bezoar, trikobezoar, Rapunzel Sendromu, çocuk

Keywords

Bezoar, trikobezoar, Rapunzel Sendromu, çocuk

Ethical Statement

Informed consent was obtained from the patient’s family.

References

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Details

Primary Language

English

Subjects

Pediatric Surgery

Journal Section

Case Report

Authors

Bilge Gördü
0000-0002-7095-7225
Türkiye

Tutku Soyer
0000-0003-1505-6042
Türkiye

Publication Date

March 31, 2024

Submission Date

September 5, 2023

Acceptance Date

November 3, 2023

Published in Issue

Year 2024 Volume: 77 Number: 1

DOI

https://doi.org/10.4274/atfm.galenos.2023.03064

IZ

https://izlik.org/JA67WH88XR

APA

Gördü, B., & Soyer, T. (2024). Rapunzel Syndrome Causing Gastric Outlet Obstruction in A 12-Year-Old Girl: Report of A Case and Review of the Literature. Ankara Üniversitesi Tıp Fakültesi Mecmuası, 77(1), 113-118. https://doi.org/10.4274/atfm.galenos.2023.03064

AMA

1.Gördü B, Soyer T. Rapunzel Syndrome Causing Gastric Outlet Obstruction in A 12-Year-Old Girl: Report of A Case and Review of the Literature. Ankara Üniversitesi Tıp Fakültesi Mecmuası. 2024;77(1):113-118. doi:10.4274/atfm.galenos.2023.03064

Chicago

Gördü, Bilge, and Tutku Soyer. 2024. “Rapunzel Syndrome Causing Gastric Outlet Obstruction in A 12-Year-Old Girl: Report of A Case and Review of the Literature”. Ankara Üniversitesi Tıp Fakültesi Mecmuası 77 (1): 113-18. https://doi.org/10.4274/atfm.galenos.2023.03064.

EndNote

Gördü B, Soyer T (March 1, 2024) Rapunzel Syndrome Causing Gastric Outlet Obstruction in A 12-Year-Old Girl: Report of A Case and Review of the Literature. Ankara Üniversitesi Tıp Fakültesi Mecmuası 77 1 113–118.

IEEE

[1]B. Gördü and T. Soyer, “Rapunzel Syndrome Causing Gastric Outlet Obstruction in A 12-Year-Old Girl: Report of A Case and Review of the Literature”, Ankara Üniversitesi Tıp Fakültesi Mecmuası, vol. 77, no. 1, pp. 113–118, Mar. 2024, doi: 10.4274/atfm.galenos.2023.03064.

ISNAD

Gördü, Bilge - Soyer, Tutku. “Rapunzel Syndrome Causing Gastric Outlet Obstruction in A 12-Year-Old Girl: Report of A Case and Review of the Literature”. Ankara Üniversitesi Tıp Fakültesi Mecmuası 77/1 (March 1, 2024): 113-118. https://doi.org/10.4274/atfm.galenos.2023.03064.

JAMA

1.Gördü B, Soyer T. Rapunzel Syndrome Causing Gastric Outlet Obstruction in A 12-Year-Old Girl: Report of A Case and Review of the Literature. Ankara Üniversitesi Tıp Fakültesi Mecmuası. 2024;77:113–118.

MLA

Gördü, Bilge, and Tutku Soyer. “Rapunzel Syndrome Causing Gastric Outlet Obstruction in A 12-Year-Old Girl: Report of A Case and Review of the Literature”. Ankara Üniversitesi Tıp Fakültesi Mecmuası, vol. 77, no. 1, Mar. 2024, pp. 113-8, doi:10.4274/atfm.galenos.2023.03064.

Vancouver

1.Bilge Gördü, Tutku Soyer. Rapunzel Syndrome Causing Gastric Outlet Obstruction in A 12-Year-Old Girl: Report of A Case and Review of the Literature. Ankara Üniversitesi Tıp Fakültesi Mecmuası. 2024 Mar. 1;77(1):113-8. doi:10.4274/atfm.galenos.2023.03064

Rapunzel Syndrome Causing Gastric Outlet Obstruction in A 12-Year-Old Girl: Report of A Case and Review of the Literature

Abstract

Keywords

Ethical Statement

12 Yaşındaki Bir Kız Çocukta Mide Çıkım Tıkanıklığına Neden Olan Rapunzel Sendromu: Olgu Sunumu ve Literatürün Gözden Geçirilmesi

Abstract

Keywords

Ethical Statement

References

Details

Primary Language

Subjects

Journal Section

Authors

Publication Date

Submission Date

Acceptance Date

Published in Issue

DOI

IZ

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