IgG4-Related Disease with Mandibular Mass and Cyst: A Case Report and Review of the Literature

Abstract

A 57 years old male patient came to our clinic with the complaint of limitation in mouth opening. There was a cystic tumor in his left mandible. A surgical approach was planned for the cyst. During the operation in the region of the masseter muscle, somewhat abnormally rigid tissues were observed. Three big tissue samples were taken from there. The histopathological diagnosis of the patient was reported as IgG4-related disease. There-upon oral corticosteroid was started on the patient without any other surgery. The patient was under control for 2 years and he is fine. It was wanted to be shared considering that it is very important to keep in mind the pathologies associated with IgG4, as it prevents the patient from an unnecessary hemimandibulectomy.

Keywords

• Mandibular Tumor
• IgG4-Related Disease
• Surgical Procedure
• Steroid Treatment

Mandibular Kitle ve Kistin Eşlik Ettiği IgG4 ile İlişkili Hastalık: Bir Olgu Sunumu ve Literatürün Gözden Geçirilmesi

Abstract

Elli yedi yaşında erkek hasta kliniğimize ağız açmada kısıtlılık şikayetiyle başvurdu. Sol mandibulada kistik tümörü mevcuttu. Kist için cerrahi tedavi planlandı. Ameliyat sırasında masseter kası bölgesinde anormal sert dokular dikkatimizi çekti. Oralardan 3 büyük doku örneği alındı. Hastanın patolojik tanısı IgG4 ile ilişkili hastalık olarak geldi. Bunun üzerine hastaya daha başka bir cerrahi planlanmaksızın oral kortikosteroid başlandı. Hasta iki yıldır kontrol altındadır ve iyidir. Hastanın gereksiz bir hemimandibulektomiye maruz kalmasının önüne geçtiği için IgG4 ile ilişkili patolojilerin akılda tutulmasının çok önemli olduğu düşünülerek paylaşılmak istendi.

Keywords

• Mandibuler Tümör
• IgG4 İle İlişkili Hastalık
• Cerrahi Tedavi
• Steroid Tedavisi

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