Karın İçi Kistik Kitle ve Obstrüktif Üropati ile Başvuran İki Yenidoğan: Vajinal Atreziye Bağlı Hidrometrokolpos

Year 2022, Volume: 75 Issue: 1, 149 - 153, 30.06.2022

Ali İhsan Anadolulu

https://doi.org/10.4274/atfm.galenos.2022.75768

Abstract

Vaginal atresia is a rare congenital anomaly and treatment approaches are varied, usually driven by symptoms. We report two newborns presenting
with an intraabdominal cystic mass and obstructive uropathy due to vaginal atresia. Physical examination revealed a mass lesion extending to the
umbilicus and lack of vaginal patency. They had polydactyly on hands and feet. Both patients underwent vaginoplasty with abdominoperineal
approach. The patients are still in the 2nd postoperative year and their follow-up is uneventful. Vaginal atresia and hydrometrocolpos should be
considered in patients with intraabdominal cystic mass and polydactyly findings.

Keywords

Vaginal Atresia , Obstructive Uropathy , Newborn

Ethical Statement

Ethics Informed Consent: Informed consent was obtained. Peer-review: Externally peer-reviewed. Financial Disclosure: The author declare that he has not received any financial support to perform this study.

References

• 1. Gupta DK, Sharma S. Hydrometrocolpos. In: Puri P, Hoellworth M (eds) Pediatric surgery: diagnosis and management
• 2. Nazir Z, Rizvi RM, Qureshi RN, et al. Congenital vaginal obstructions: varied presentation and outcome. Pediatr Surg Int. 2006;22:749-753.
• 3. Ekenze SO, Ezegwui HU. Hydrometrocolpos from a low vaginal atresia: an uncommon cause of neonatal intestinal and urinary obstruction. Afr J Paediatr Surg. 2008;5:43-45.
• 4. Kimble R, Molloy G, Sutton B. Partial Cervical Agenesis and Complete Vaginal Atresia. J Pediatr Adolesc Gynecol. 2016;29:e43-e47.
• 5. Sánchez-Ferrer ML, Acién MI, Sánchez del Campo F, et al. Experimental contributions to the study of the embryology of the vagina. Hum Reprod. 2006;21:1623-1628.
• 6. Louden ED, Awonuga AO, Gago LA, et al. Rare Müllerian Anomaly: Complete Septate Uterus with Simultaneous Longitudinal and Transverse Vaginal Septa. J Pediatr Adolesc Gynecol. 2015;28:e189-e191.
• 7. Benson CB, Doubilet PM. The fetal genitourinary system. In: Fleischer AC, editor. Sonography in Obstetrics and Gynecology. London: Prentice-Hall International; 1996. s. 444-450.
• 8. Lim YH, Ng SP, Jamil MA. Imperforate hymen: report of an unusual familial occurrence. J Obstet Gynaecol Res. 2003;29:399-401.
• 9. El-Messidi A, Fleming NA. Congenital imperforate hymen and its lifethreatening consequences in the neonatal period. J Pediatr Adolesc Gynecol. 2006;19:99-103.
• 10. Anguenot JL, Ibecheole V, Salvat J, et al. Hematocolpos secondary to imperforate hymen, contribution of transrectal echography. Acta Obstet Gynecol Scand. 2000;79:614-615.
• 11. Messina M, Severi FM, Bocchi C, et al. Voluminous perinatal pelvic mass: a case of congenital hydrometrocolpos. J Matern Fetal Neonatal Med. 2004;15:135-137.
• 12. Shaked O, Tepper R, Klein Z, et al. Hydrometrocolpos--diagnostic and therapeutic dilemmas. J Pediatr Adolesc Gynecol. 2008;21:317-321.