Mesenteric Vein Thrombosis Due to Protein S Deficiency in a Girl
Abstract
Mesenteric venous thrombosis (MVT) is a very rare condition in children, and may cause bowel infarction and gangrene. It may be caused by congenital or acquired factors, including protein S deficiency; a very rare genetic disorder. Here we report a case of MVT in a girl with protein S deficiency. The patient developed splenic necrosis and massive small bowel infarction sparing the colon. Contrast enhanced computed tomography led to prompt diagnosis of small bowel and splenic necrosis. The patient was treated successfully by resection of the necrotic bowel and anticoagulant therapy.
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References
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