Posmortem Tanı Alan Familyal Eritrofagositik Lenfohistiositozis Olgusu
Abstract
Ateş, hepatosplenomegali, anemi ve trombositopeni nedeniyle izlenerek kısa sürede kaybedilen ve otopsi ile FEL tanısı alan 4 aylık erkek hasta takdim edildi ve hastalığın klinik ve laboratuvar bulguları gözden geçirilerek ayırıcı tanısı tartışıldı.
Keywords
FEL, Ateş, hepatosplenomegali, anemi ve trombositopeni
Familial Erythrephagoeytic Lymphohistiocytosis Diagnosed by Postmortem Examination
Abstract
A four - month old boy who had sysmptoms of fever, hepatosplenomegalie, anemia, and thrombocytopenia is presented. He died in a short course and post mortem examination revealed the diagnosis of FEL. The symptoms, clinical course, laboratory findings and differantial diagnosis of the disease were reviewed.
Keywords
FEL, Fever, hepatosplenomegaly, anemia and thrombocytopenia