Posmortem Tanı Alan Familyal Eritrofagositik Lenfohistiositozis Olgusu

Year 1990, Volume: 43 Issue: 4, 1025 - 1032, 31.12.1990

Sevgi Başkan

https://izlik.org/JA56AU83YR

Abstract

Ateş, hepatosplenomegali, anemi ve trombositopeni nedeniyle izlenerek kısa sürede kaybedilen ve otopsi ile FEL tanısı alan 4 aylık erkek hasta takdim edildi ve hastalığın klinik ve laboratuvar bulguları gözden geçirilerek ayırıcı tanısı tartışıldı.

Keywords

FEL , Ateş , hepatosplenomegali , anemi ve trombositopeni

Familial Erythrephagoeytic Lymphohistiocytosis Diagnosed by Postmortem Examination

https://izlik.org/JA56AU83YR

Abstract

A four - month old boy who had sysmptoms of fever, hepatosplenomegalie, anemia, and thrombocytopenia is presented. He died in a short course and post mortem examination revealed the diagnosis of FEL. The symptoms, clinical course, laboratory findings and differantial diagnosis of the disease were reviewed.

Keywords

FEL , Fever , hepatosplenomegaly , anemia and thrombocytopenia

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