Posmortem Tanı Alan Familyal Eritrofagositik Lenfohistiositozis Olgusu

Abstract

Ateş, hepatosplenomegali, anemi ve trombositopeni nedeniyle izlenerek kısa sürede kaybedilen ve otopsi ile FEL tanısı alan 4 aylık erkek hasta takdim edildi ve hastalığın klinik ve laboratuvar bulguları gözden geçirilerek ayırıcı tanısı tartışıldı.

Keywords

• FEL
• Ateş
• hepatosplenomegali
• anemi ve trombositopeni

Familial Erythrephagoeytic Lymphohistiocytosis Diagnosed by Postmortem Examination

Abstract

A four - month old boy who had sysmptoms of fever, hepatosplenomegalie, anemia, and thrombocytopenia is presented. He died in a short course and post mortem examination revealed the diagnosis of FEL. The symptoms, clinical course, laboratory findings and differantial diagnosis of the disease were reviewed.

Keywords

• FEL
• Fever
• hepatosplenomegaly
• anemia and thrombocytopenia

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