Budd-Chiari Syndrome: Analysis of 10 Cases
Abstract
10 Patients, out of 13,859 patients who were admitted to the Gastroenterology Departement of Faculty of Medicine, University of Ankara, from 1964 - through 1978, were diagnosed to have Budd-Chiari Syndrome.Five of the patients were male and the other 5 were female and the avarage age was 28 years. In our subjects, the time between the start of symptoms and the diagnosis was found to be 64 months. When the subjects were admitted to the hospital they complained of tiredness (20 70), abdominal pain (30 70), fever (30 70), edema in lower extremities (60 70), palpitation (10 0/0), dyspnea (10 0/0), abdominal distension (90 70).
In 90 % of our subjects hepatomegaly, in 80 % splenomegaly, in 80 % ascites, in 100 % collateral venous circulation, in 60 % edema in lower extremites, in 10 % jaundice and in 10 % hemorrhagic pleural effusion were observed. In 80 % of our subjects, obstruction of vena cava inferior, which were tought to be due to trombosis, was found. The symptoms occured in the sixth month of the pregnancy in one case and in another case in puerperium. In another subject polycythemi and leukocytosis were present. In 7 cases the etiology was either unknown or inadequately established.
Keywords
lower extremity edema, collateral venous circulation, hemorrhagic pleural effusion
References
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