Budd - Chiari Sendromu : 10 Olgunun Analizi

Year 1980, Volume: 33 Issue: 3, 353 - 364, 30.09.1980

Ali Özden

Abstract

A. Ü. T. Fakültesi Gastroenteroloji kliniğine 1964 - 1978 yılları arasında yatan 13,859 hastanın 10 u Budd-Chiari sendromu tanısı almıştır (% 0,07). 10 olgunun 5 i kadın, 5 i erkek ve yaş ortalaması 28 dir. Olgularımızda semptomlarm başlaması ile tanı konuncaya kadar geçen süre 64 ay olarak bulundu. Ol363 gulanmmn bize vurduklarrnda yaklnmlarr, halsizlik ( % 20), karm liži ( % 90), alt ekstremitelerde ödem ( % 60), ( % 30), karm aEr1S1 ( % 30), palpitasyon ( % 10), dyspne ( % 10) idi. Olgulanmmn % 90 mnda hepatomegali, % 80 ninde splenomegali, % 80 ninde asit, % 100 tinde kollateral venöz dolapm, % 60 Inda alt ekstremitelerde ödem, % 10 unda sarlllk, % 10 nunda hemorajik plevral epanynan mevcut idi. Olgularlmrzan % 80 ninde vena cava inferiorda trombusa bažll oldužunu dihündüEümüz obstruksiyon saptandl. Olgulanrmzrn birinde semptomlar gebeližin 6 Incr aymda, bir diEerinde puerperyumda ortaya Olgulanmmn birinde polisitemi ve lökositoz vardl. Yedi olguda ise sorumlu tutulabilecek etyolojik faktör tesbit edemedik.

Keywords

lower extremity edema , collateral venous circulation , hemorrhagic pleural effusion

Budd-Chiari Syndrome: Analysis of 10 Cases

Abstract

10 Patients, out of 13,859 patients who were admitted to the Gastroenterology Departement of Faculty of Medicine, University of Ankara, from 1964 - through 1978, were diagnosed to have Budd-Chiari Syndrome.Five of the patients were male and the other 5 were female and the avarage age was 28 years. In our subjects, the time between the start of symptoms and the diagnosis was found to be 64 months. When the subjects were admitted to the hospital they complained of tiredness (20 70), abdominal pain (30 70), fever (30 70), edema in lower extremities (60 70), palpitation (10 0/0), dyspnea (10 0/0), abdominal distension (90 70).
In 90 % of our subjects hepatomegaly, in 80 % splenomegaly, in 80 % ascites, in 100 % collateral venous circulation, in 60 % edema in lower extremites, in 10 % jaundice and in 10 % hemorrhagic pleural effusion were observed. In 80 % of our subjects, obstruction of vena cava inferior, which were tought to be due to trombosis, was found. The symptoms occured in the sixth month of the pregnancy in one case and in another case in puerperium. In another subject polycythemi and leukocytosis were present. In 7 cases the etiology was either unknown or inadequately established.

Keywords

lower extremity edema , collateral venous circulation , hemorrhagic pleural effusion

References

• 1. Barge J, Mingot J, Potet F : Les aspects anatomo-pathologiques deg syndromes de Budd-Chiari, aigus et chroniques. A propos de cinq observations, Sem Hôp Paris 47 : 2987, 1971
• 2. Beaugrand M, Matuchansky C, Ferrier J-P : Syndrome de Budd-Chiari revelateur d'un cancer du rein, Arch Fr Mal App Dig 64 : 331, 1975
• 3. Bigot JM, Chermet J, Monnier J-P : Les syndromes de Budd-Chiari diagnostiques radiologiques, Ann Radiol 17 : 451, 1974
• 4. Caroli J, Guille C : Diagnostic scintigraphique et arteriographique du syndrome de Budd-Chiari, Rev Med Chir Mal Foie 5 : 211, 1971
• 5. Clauvel J-P, Chassigneux J, Seligmann M : L'association polyglobulie. Syndrome de Budd-Chiari, La Presse Medicale 4 : 189, 1967
• 6. Hoyumpa AM, Schiff L, Helfman EL : Budd-Chiari syndrome in women taking oral contraceptives, J Amer Med 50 : 137, 1971
• 7. Job C ve ark : Exploration radiologique du -syndrome de Budd-Chiari, La Nouvelle Presse Medicale 12 : 1021, 1977
• 8. Levy VG, Caroli J : Syndrome de Budd-Chiari, Med Chir Dig 3 : 389, 1974
• 9. Oettinger ve ark : Budd-Chiari syndrome in pregnancy, J Obstet Gynec Brit Comm 77 : 174, 1970
• 10. Paraf A ve ark Les obstructions du segment inter-hepato-cardiaque de la veine cave inferieure, Rev Med Chir Mal Foie 44 : 39, 1969
• 11. Parker RG F : Occlusion of the hepatic veins in man, Medicine (Baltimore) 38 : 369, 1959
• 12. Piwnica A ve ark : Valves et membranes anormales de la veine cave inferieure terminaie, J Chir 96 : 45, 1968
• 13. Takeuchi J ve ark : Budd-Chiari syndrome associated With obstruction of the inferior vena cava, Amer J Med 15 : 11, 1971
• 14. Tavill AA ve ark : Liver physiology and disease : 'The Budd-Chiari syndrom : Correlation between hepatic scintigraphy and the clinical radiological and pathological finding in nineteen cases of hepatic venous out flow obstruction, Gastroenterology 68 509, 1975
• 15. Thomas M, Caroli J : Le syndrome de Budd-Chiari. Revue de la litterature. A propos de 21 observations, Rev Med Chir Mal Foie 44 : I, 1969