A Rare Form of Amyloidosis: Tracheobronchial Amyloidosis

Year 2016, Volume: 18 Issue: 3, 106 - 109, 01.12.2016

Ceyhan Uğurluoğlu Ercan Kurtipek Yaşar Ünlü Nur Düzgün

Abstract

Primary isolated tracheobronchial amyloidosis(TBA) is a quite common disease. The symptomsof TBA are progressive dyspnoea, cough, and hemoptysis. It can lead to airway obstruction,atelectasia, and repetitive bronchopulmonary infections. The present case was a male patientdelivered to the emergency service with disorders in general medical condition and washospitalized in the thoracic disorders department due to coughing, sputum, and labored breathingwith a 15 year history of Parkinson disease. No significant pathologies were evident in chestX-ray image. The computer tomography imager revealed; however, in the lower lobe of theright lung posterior-basal and lateral-basal segment large scale consolidations. There was apolyploidy lesion in the upper left lobe carina visible in the bronchoscopy made. The biopsytaken was diagnosed as amyloidosis. As there was no other organ involvement determined, thepresent case is diagnosed as isolated tracheobronchial amyloidosis

Keywords

Amyloidosis, lung, kongo red

AMİLOİDOZUN NADİR BİR FORMU: TRAKEOBRONŞİYAL AMİLOİDOZİS

Abstract

Primer izole trakeobronşiyal amiloidozis (TBA), oldukça nadir görülen bir hastalıktır.Progressif dispne, öksürük ve hemoptizi gibi semptomlarla kendini gösterebilir. Hava yoluobsrtrüksiyonu, atelektazilere ve tekrarlayan bronkopulmoner enfeksiyonlara neden olabilir.Soliter nodüller tümör benzeri yanıltıcı görünümler verebilir. 70 yaşında erkek hasta genel durumbozukluğu öksürük, balgam, nefes darlığı şikayeti ile acil servise başvurdu ve göğüs hastalıklarıservisine yatırıldı. 15 yıldır parkinson hastalığı olan hastamızın akciğer filminde belirgin birpatoloji tesbit edilmedi. BT Toraks’da sağ akciğer alt lob posterobazal ve laterobazal segmenttegeniş boyutlu konsolidasyon alanı mevcuttu. Yapılan bronkoskopide sol üst lob karinasındapolipoid lezyon görüldü. Alınan bronkoskopik biyopsi örneği amiloidoz olarak raporlandı. Başkaorgan tulumu saptanmayan izole TBA’ lı olgumuzu literatür eşliğinde sunmayı amaçladık

Keywords

Amiloidoz, akciğer, kongo kırmızısı

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