Soft and Hard Tissue Changes in the Oral and Maxillofacial Region in Patients with Neurofibromatosis: Rare Case Report

Yıl 2023, Cilt: 2 Sayı: 1, 14 - 15, 20.01.2023

Günay Yapıcı Yavuz , Mahmut Koparal , Aydın Keskinrüzgar , Seyma Bayazıt

Öz

Introduction
Neurofibromatosis is a group of autosomal dominant genetic disorders characterized by multiple cutaneous lesions and tumors
of the nervous system. NF is categorized into two, NF type-1 and NF type-2. Neurofibromatosis-1 is a neurocutaneous-skeletal
disorder with variable phenotypic description. Craniofacial skeletal symptoms of the disease are observed in the jaw deformations
and impacted, missing and displaced teeth can also be seen. The purpose of this report is to present a case of NF1.
Case report
A 23-year-old male patient was referred to the Department of Maxillofacial Surgery, Faculty of Dentistry, Adiyaman University
due to abscess of molar teeth. As a result of the panoramic radiography taken from the patient, the second and third molar teeth
were impacted in the left mandibula.
Conclusion
In neurofibromatosis, bone and soft tissue involvement can be seen in the maxillofacial region. They are also lesions that can
cause the impacted teeth.

Anahtar Kelimeler

Neurofibromatosis, maxillofacial region, autosomal dominant

Kaynakça

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