Hücresel Varyantlı Serebellar Hemangioblastoma: Bir Olgu Sunumu

Year 2024, Volume: 5 Issue: 3, 122 - 124, 30.11.2024

Ömer Polat , Bartu Soysal , Hamza Karabudak , Bengü Göksular , Canberk Topuz , Barıs Chouseın , Gülşah Özdemir , Ebru Taştekin

Abstract

Hemanjioblastom oldukça vaskülarize, yavaş büyüyen, berrak, vakuollü sitoplazma ve spesifik immünohistokimyasal boyama özellikleri ile tanı koyulan, neoplastik stromal hücreler içeren derece 1 tümörlerdir. Hemanjiyoblastomlar beyinde, omurilikte veya retinada ortaya çıkabilir ve tüm intrakranyal tümörlerin yaklaşık %1-2,5' unu oluşturur. Baş ağrısı ve glokom şikayetiyle hastanemize başvuran 36 yaşında erkek hastayı sunduk. Hastanın radyolojik görüntülerinde sağ posterior fossada lokalize beyin kitlesi görüldü. Cerrahi rezeksiyon sonrası patolojik değerlendirme yapıldı ve hastaya selüler hemanjiyoblastom tanısı konuldu. Yaklaşık iki ay kadar yoğun bakımda takip edilen hasta maalesef tümör dışı nedenlere bağlı kalp-akciğer durması nedeniyle hayatını kaybetti.

Keywords

Hemanjiyoblastom , serebellum , vasküler neoplazm

Cellular Variant Cerebellar Hemangioblastoma: A Case Report

Abstract

Hemangioblastoma is a highly vascularized, have a slow-growing rate grade 1 tumor which are containing neoplastic stromal cells with clear, vacuolated cytoplasm and diagnosed with specific immunohistochemical staining features. Hemangioblastomas can occur in the brain, spinal cord or retina and they account for about 1-2.5% of all intracranial tumors. We presented a 36-year-old male patient presented with a headache and glaucoma. In the radiological images, a cerebellar mass was observed in the localization of the right middle cerebellar pedincle. After surgical resection pathological evaluation was done and as a result, the patient was diagnosed as cellular hemangioblastoma. He was followed up in the intensive care unit for about two months and unfortunately died due to the cardiopulmonary arrest associated with non-tumoral reasons. This case report was a descriptive example for a rare variant of a rare cerebellar tumors

Keywords

hemangioblastoma , cerebellum , vascular neoplasm

Ethical Statement

In the preparation of this report, the confidentiality and confidentiality of the patient was protected at the highest level and the principles of medical ethics were fully complied with. Since the patient died, the necessary consent was obtained from his relatives.

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