The management of Bochdalek congenital diaphragmatic hernia: a single center experience and review of the literature

Year 2020, Volume: 6 Issue: 2, 138 - 144, 04.03.2020

Sefer Tolga Okay Serpil Sancar , Esra Özçakır , İpek Güney Varal Pelin Doğan Mete Kaya

https://doi.org/10.18621/eurj.467162

Cited By: 1

Abstract

Objectives:
Congenital diaphragmatic hernia (CDH) is a rare congenital anomaly of the
diaphragm with pulmonary hypoplasia and persistent pulmonary hypertension and
has serious consequences. Despite recent diagnosis and treatment strategies,
CDH is still a challenging condition. We aim to present our clinical
experiences of CDH, and review of the literature.

Methods: Data of
CDH patients who were operated in our clinic between January 2010 and September
2018 were obtained from the patient's chart. The clinical course and results of
the patients with Bochdalek type CDH were reviewed.

Results: We
performed diaphragmatic closure in 16 patients with Bochdalek CDH during study
period. Fourteen (82%) cases were diagnosed antenatally. In 5 (29%) patients,
preoperative pulmonary hypertension developed and nitric oxide was
administered. Twelve of the sixteen patients (75%) underwent primary repair and
4 of them underwent prosthetic patch. Three patients were repaired
thoracoscopically. Five (31%) patients died due to severe persistent pulmonary
hypertension on postoperative period. There was no recurrence in our patients
who were followed-up for a mean of 27 months.

Conclusion: In
the management of Bochdalek CDH, the clinical success has been increasing in
parallel with the important developments with the application of new treatment
modalities in the neonatal intensive care units and new surgical techniques in
recent years.

Keywords

Bochdalek hernia, congenital diaphragmatic hernia, newborn, pulmonary hypertension

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