Wunderlich's syndrome as the fatal complication of a renal angiomyolipoma: a case report and review of the literature

Year 2019, , 153 - 155, 22.09.2019

Fatma Zeynep Arslan , Ayşegül Altunkeser

https://doi.org/10.32322/jhsm.496356

Abstract

Wunderlich
syndrome (WS) is a rare acute abdominal condition, which is  characterized with spontaneous nontraumatic
renal haemorrhage into the subcapsular and perirenal spaces. Renal cell
carcinoma, angiomyolipoma, renal cysts, vasculitis or blood dyscrasias are
among the known risk factors. We
report a case of Wunderlich's syndrome in an 59 year old woman associated with
massive retroperitoneal hemorrhage.

Keywords

Wunderlich syndrome, angiomyolipoma, computed tomography

Renal anjiyomiyolipomun ölümcül komplikasyonu olarak Wunderlich sendromu: olgu sunumu ve literatürün gözden geçirilmesi

Abstract

Wunderlich sendromu (WS), subkapsüler ve perirenal boşluklara nonumumatik renal kanama ile ilişkili nadir bir akut karın hastalığıdır. Renal hücreli karsinom, anjiyomiyolipom, böbrek kistleri, vaskülit veya kan disprasileri bilinen risk faktörleri arasındadır. Masif retroperitoneal kanama ile ilişkili 59 yaşındaki bir kadın hastada Wunderlich sendromu olgusunu sunuyoruz.

Keywords

Wunderlich sendromu, anjiyomiyolipom, bilgisayarlı tomografi

References

• 1. Katabathina VS, Katre R, Prasad SR. Wunderlich syndrome: cross-sectional imaging review. J Comput Assist Tomogr. 35 (4): 425-33. doi:10.1097/RCT.0b013e3182203c5e
• 2. Rakowski SK, Winterkorn EB, Paul E, Steele DJ, Halpern EF, Thiele EA. Renal manifestations of tuberous sclerosis complex: Incidence, prognosis and predictive factors. Kidney Int 2006;70:1777-82.
• 3. Ramon J., Rimon U., Garniek A. “ZARenal angiomyolipoma: long-term results following selective arterial embolization,” European Urology, vol. 55, no. 5, pp. 1155–1162, 2009
• 4. Kim JW, Kim JY, Ahn ST, Park TY, Oh MM, Moon DG, Park HS. Spontaneous perirenal hemorrhage (Wunderlich syndrome): An analysis of 28 cases. The American journal of emergency medicine, 2018.
• 5. Medda M, Picozzi SC, Bozzini G, Carmignani L. Wunderlich’s syndrome and hemorrhagic shock. Journal of Emergencies, Trauma and Shock. 2009;2(3):203-205. doi:10.4103/0974-2700.55346.