Nadir bir tibia'da adamantinoma olgusu, radyolojik özellikleri

Abstract

Adamantinoma, nadir görülen düşük dereceli primer malign kemik tümörüdür ve genellikle tibia diyafizinde bulunur. Tümör lokal olarak agresiftir ve metastaz yapabilir. Kemoterapi ve radyoterapiye dirençli olduğu için asıl tedavi lezyonun geniş cerrahi sınırlarla total eksizyonudur. Radyolojik olarak diğer kemik lezyonlarından (osteofibröz displazi gibi) ayırt etmek zor olsa da bazı ayırt edici özellikleri vardır. Tipik bir vakanın bu sunumu ile radyologların dikkatini bu lezyona çekmeyi umuyoruz.

Keywords

• ADAMANTİNOMA
• TİBİA
• KEMİK NEOPLAZMLARI
• RADYOLOJİ
• MRG
• OSTEOFİBRÖZ DİSPLAZİ

A rare case of adamantınoma ın tıbıa and radıologıcal features

Abstract

Adamantinoma is a rare low grade primary malignant bone tumor. The tumor is usually located in the diaphysis of tibia. The tumor is locally aggressive and can metastasis. As it is resistant to chemotherapy and radiotherapy, the main treatment is total excision of the lesion with wide surgical margins. Although it is difficult to distinguish from other bone lesions (such as osteofibrous dysplasia) radiologically, there are some helpful features. With this presentation of a typical case, we hope to draw the attention of radiologists to this lesion.

Keywords

• ADAMANTINOMA
• TIBIA
• BONE NEOPLASMS
• RADIOLOGY
• MRI
• OSTEOFIBROUS DYSPLASIA

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