Erişkin bir hastada çift odacıklı sağ ventrikül ve ciddi koroner arter hastalığı: Olgu sunumu

Abstract

Çift odacıklı sağ ventrikül, anormal gelişmiş kas bantlarının sağ
ventrikülü iki parçaya böldüğü konjenital bir kardiyak anomalidir.
Kırk altı yaşında erkek hastada çift odacıklı sağ venrtikül, biküspid
aort kapak ve ciddi koroner arter hastalığı tespit edilerek cerrahi
girişime karar verildi. Operasyonda sağ ventrikülotomi yoluyla
obstrüksiyona sebep olan anormal adale bantları rezeke edildi.
İnfundibular darlık Gore-tex yama ile genişletildi. İlave olarak sol
internal torasik arter ile sol ön inen koroner artere bypass girişimi
uygulandı. Erişkin hasta popülasyonunda, çift odacıklı sağ ventrikül
ile koroner arter hastalığı birlikteliği son derece nadir olup
sunduğumuz olgu literatür taramasından elde ettiğimiz bilgiye göre,
bildirilen üçüncü olgudur.

Keywords

• Erişkin çağ, Çift odacıklı sağ ventrikül, Pulmoner hipertansiyon

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Abstract

Double-chambered right ventricle is a congenital cardiac anomaly in which the right ventricle is divided into two portions by anomalous muscle bundles. We discuss a patient aged 46 who had a double-chambered right ventricle, with coronary artery stenosis and a bicuspid valve. Our patient underwent successful surgical resection of the obstruction by a right ventriculotomy and the infundibular stenosis was expanded with a Gore-tex patch. Also, a left internal mammary artery-left anterior descending coronary artery anostomosis was performed for the left anterior descending stenosis. Although, double-chambered right ventricles are extremely rare in adults, the example of double-chambered right ventricle with coronary artery stenosis which we diagnosed and operated on was the third case reported according to our review of the literature.

Keywords

• Adulthood, Double-chambered right ventricle, Pulmonary hypertension

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