COCHLEAR IMPLANTATION IN A PATIENT WITH USHER'S SYNDROME

Yıl 2002, Cilt: 15 Sayı: 4, 258 - 261, 03.12.2016

Ufuk Derinsu Ayca Ciprut

Öz

Usher's Syndrome is an autosomal recessive disorder characterized by congenital hearing loss and retinitis pigmentosa. Usher’s Syndrome patients with severe to profound sensorineural hearing loss can be considered as candidates for cochlear implantation.
This case study reports a deaf-blind with Usher's Syndrome who received a cochlear implant, the audiological evaluation is presented and the therapy sessions are discussed. The patient demonstrated good performance overtime after the implantation including open set speech understanding and telephone use.
Key Words : Usher's Syndrome, Cochlear implant

Kaynakça

• I. Oorlin RJ. Genetic hearing loss with eye disorders. In: Gorlin RJ, Toriello 11V, Cohen MM, eds. Hereditary Hearing Loss and Its Syndromes.Hew York: Oxford University
• Rress, 1995:105-140.
• Young HM, Johnson JC, Mets MB, Hain TC. Cochlear implants in young children with Usher's Syndrome. Ann Otol Rhinol Laiyngol (Suppl), 1995 ; 166:542-345.
• Hinderink JB, Brokx JPL, Mens LH, Van Den Broek P. Results from four cochlear implant patients with Ushers Syndrome. Ann Otol Rhinol Laryngol 1994:103:285-293.
• Saeed SR, Ramsden RT, Axon PR. Cochlear implantation in the deaf-blind.Am J Otol 1998; 19:774-777.