Neuro-Behçet Disease Presenting with Sinus Venous Thrombosis: Case Report

Year 2017, Volume: 18 Issue: 3, 215 - 218, 31.12.2017

Hesna Bektaş , Şadiye Temel Orhan Deniz Hava Dönmez Keklikoğlu , Gönül Vural

Abstract

Behçet’s disease (BD) is a rare, chronic, autoimmune, autoinflammatory disorder of unknown origin. Mucocutaneous lesions and panuveitis constitute the hallmark of Behçet's. The disease is mostly seen at the third decade and disease course is dramatically more severe for males than females. Vascular involvement can occur in up to 40% of the cases. Although veins are mostly involved, all sizes and types of vessels can be affected. The most common clinical presentation of disease is lower extremity vein thrombosis. Vena cava thrombosis, pulmonary artery aneurysms, Budd-Chiari syndrome, peripheral artery aneurysms, dural sinus thrombosis and abdominal aorta aneurysms are also frequent at the disease’s course. Prevalence of cerebral venous thrombosis is 8%. In this article, we presented a 28-year-old man with sinus venous thrombosis due to BD.

Keywords

Behçet disease , sinus venous thrombosis , headache

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