General anesthesia application with the patient who has kabuki make-up syndrome

Ferhunde Dilek Subaşı; Sami Yarkın Sözüer; Hilal Akça; Osman Ekinci

EN

General anesthesia application with the patient who has kabuki make-up syndrome

Abstract

Kabuki Syndrome is disease derived from a rare genetic mutation that is particularly characterized by distinctive facial features, musculosketal malformations, mental retardation and cardiopulmonary anomalies and several pathologies. From anesthetic aspect, this syndrome may cause both cardiovascular and inspiratory problems, defects in palate and collum and also a number of difficulties in selecting medications and invasive procedures. Difficult intubation, prolonged neuromuscular blockage and malignant hyperthermia are frequently encountered problems in the patients with Kabuki Syndrome. An attentive examination of the patient in preoperative stage and appropriate medication preference is essential in order to prevent complications.

Keywords

References

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Details

Primary Language

English

Subjects

Health Care Administration

Journal Section

Case Report

Authors

Ferhunde Dilek Subaşı This is me
0000-0003-3269-9138
Türkiye

Sami Yarkın Sözüer This is me
0000-0002-5251-7664
Türkiye

Hilal Akça ^*
0000-0003-4875-9166
Türkiye

Osman Ekinci
0000-0002-7891-1774
Türkiye

Publication Date

March 18, 2022

Submission Date

September 4, 2021

Acceptance Date

February 17, 2022

Published in Issue

Year 2022 Volume: 39 Number: 2

IZ

https://izlik.org/JA58RS75CX

Cite

RIS / Bibtex

APA

Subaşı, F. D., Sözüer, S. Y., Akça, H., & Ekinci, O. (2022). General anesthesia application with the patient who has kabuki make-up syndrome. Deneysel Ve Klinik Tıp Dergisi, 39(2), 560-562. https://izlik.org/JA58RS75CX

AMA

1.Subaşı FD, Sözüer SY, Akça H, Ekinci O. General anesthesia application with the patient who has kabuki make-up syndrome. J. Exp. Clin. Med. 2022;39(2):560-562. https://izlik.org/JA58RS75CX

Chicago

Subaşı, Ferhunde Dilek, Sami Yarkın Sözüer, Hilal Akça, and Osman Ekinci. 2022. “General Anesthesia Application With the Patient Who Has Kabuki Make-up Syndrome”. Deneysel Ve Klinik Tıp Dergisi 39 (2): 560-62. https://izlik.org/JA58RS75CX.

EndNote

Subaşı FD, Sözüer SY, Akça H, Ekinci O (March 1, 2022) General anesthesia application with the patient who has kabuki make-up syndrome. Deneysel ve Klinik Tıp Dergisi 39 2 560–562.

IEEE

[1]F. D. Subaşı, S. Y. Sözüer, H. Akça, and O. Ekinci, “General anesthesia application with the patient who has kabuki make-up syndrome”, J. Exp. Clin. Med., vol. 39, no. 2, pp. 560–562, Mar. 2022, [Online]. Available: https://izlik.org/JA58RS75CX

ISNAD

Subaşı, Ferhunde Dilek - Sözüer, Sami Yarkın - Akça, Hilal - Ekinci, Osman. “General Anesthesia Application With the Patient Who Has Kabuki Make-up Syndrome”. Deneysel ve Klinik Tıp Dergisi 39/2 (March 1, 2022): 560-562. https://izlik.org/JA58RS75CX.

JAMA

1.Subaşı FD, Sözüer SY, Akça H, Ekinci O. General anesthesia application with the patient who has kabuki make-up syndrome. J. Exp. Clin. Med. 2022;39:560–562.

MLA

Subaşı, Ferhunde Dilek, et al. “General Anesthesia Application With the Patient Who Has Kabuki Make-up Syndrome”. Deneysel Ve Klinik Tıp Dergisi, vol. 39, no. 2, Mar. 2022, pp. 560-2, https://izlik.org/JA58RS75CX.

Vancouver

1.Ferhunde Dilek Subaşı, Sami Yarkın Sözüer, Hilal Akça, Osman Ekinci. General anesthesia application with the patient who has kabuki make-up syndrome. J. Exp. Clin. Med. [Internet]. 2022 Mar. 1;39(2):560-2. Available from: https://izlik.org/JA58RS75CX