Delayed diagnosis of selective immunoglobulin deficiency: A case report

Year 2016, Volume: 33 Issue: 3, 175 - 177, 06.01.2017

Veysel Kars Tahsin Celepkolu Ahmet Yilmaz Fatih Esmer Sevdegul Karadas

Abstract

Selective immunoglobulin A deficiency (SIgAD) is the most common of all primary immunodeficiency diseases; however, the pathogenesis has not been fully understood. Although most people with SIgAD are asymptomatic, some may present with recurrent infections; such as respiratory disorders, gastrointestinal tracts disorders, and allergic disorders. Herein, we report a case with SIgAD who presented with the complaints of pruritus, dental caries and chronic sinopulmonary infections.

Keywords

Pruritus, Recurrent infections, Selective immunoglobulin a deficiency, Sinopulmonary infections

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