Giant desmoid tumor in the neck

Abstract

Desmoid tumor is a benign tumor which originates from musculoaponeurotic system, can reach greater sizes with local invasion among facial plans, and cause severe deformities, morbidity and even mortality by compression of adjacent structures. These tumors are rarely seen in the head and neck region. The treatment of advanced desmoid tumors of head and neck region is surgery and radiotherapy. In this paper, we present -to the best of our knowledge- the greatest desmoid tumor case of the head and neck region in the literature.

Keywords

• Aggressive fibromatosis, radiotherapy, surgery

Boyunda dev desmoid tümör

Abstract

Desmoid tümör muskuloaponevrotik sistemden köken alan, fasiyal planlar arasında lokal yayılarak büyük boyutlara ulaşabilen, çevre yapılara bası yaparak ciddi deformitelere, morbiditeye ve hatta mortaliteye neden olabilen iyi huylu bir tümördür. Bu tümörler baş ve boyun bölgesinde nadir görülür. İlerlemiş baş ve boyun bölgesi desmoid tümörlerin tedavisi cerrahi ve radyoterapidir. Bu yazıda, bildiğimiz kadarıyla literatürdeki en büyük baş ve boyun bölgesi desmoid tümör olgusu sunuldu

Keywords

• Agresif fibromatozis, radyoterapi, cerrahi

References

1. Dalen BP, Bergh PM, Gunterberg BU. Desmoid tumors: a clinical review of 30 patients with morethan 20 years' follow-up. Acta Orthop Scand 2003;74:455-9.
2. Lessow AS, Song P, Komısar A. Unusual fibromatosis of the head and neck. Otolaryngol Head Neck Surg 2004;3:366-9.
3. Abdelkader M, Riad M, Williams A. Aggressive fibromatosis of the head and neck (desmoid tumors): review. J Laryngol Otol 2001;115:772-6.
4. Fletcher CDM. Myofibroblastic tumours: an update. Verh Dtsch Ges Path 1998;82:75-82.
5. Shields CJ, Winter DC, Kirwan WO, Redmond HP. Desmoid tumours. Eur J Surg Oncol 2001;278:701-6.
6. Klemmer S, Pascoe L, DeCosse J. Occurence of desmoids in patients with familial adenomatous polyposis of the colon. Am J Med Gent 1987;282:385-92.
7. Wilcken N, Tattersall MH. Endocrine therapy for desmoid tumors. Cancer 1991;68:1384-8.
8. Eagel BA, Zentler MP, Smith IE. Mesenteric desmoid tumours in Gardner's syndrome: review of medical treatments. Postgradmed J 1989;65:497-501.

9. Kingston CA, Owens CM, Jeanes A, Malone M. Imaging of desmoid fibromatosis in pediatric patients. Am J Roentgenology 2002;178:191-9.
10. El-Haddad M, El-Sebaie M, Ahmad R, Khalil E, Shahin M, Pant R, et al. Treatment of aggressive fibromatosis: the experience of a single institution. Clin Oncol (R Coll Radiol) 2009;21:775-80.