Nüks dev retroperitoneal liposarkom: Olgu sunumu ve literatürün gözden geçirilmesi

Abstract

Retroperitoneal sarkomlar tüm yumu­şak doku sarkomlarının % 15’ini oluşturan nadir tümörlerdir. Sıklıkla insidental olarak tanı alan retroperitoneal sarkomlarda en sık rastlanan histolojik tip liposarkomdur. Ret­roperitoneal liposarkomlarda yaşam süresini uzatan majör tedavi şekli geniş cerrahi re­zeksiyondur. Cerrahi sonrası lokal rekürrens ve metastaz riskinden dolayı bu hastaların multidispliner olarak uzun dönem takip edil­meleri gerekmektedir. Burada ilk operasyo­nu sonrası takipsiz kalan ve 16 yıl sonra 24 cm’lik dev retroperitoneal kitle ile başvuran 72 yaşındaki bir liposarkom olgusuna yakla­şımımızı sunduk.

Keywords

• liposarkom,nüks,retroperiton

Recurrence giant retroperitoneal liposarcoma: A case report and review of the literature

Abstract

Retroperitoneal sarcomas are rare tumors and form 15% of all soft tissue sarcomas. The most common histologic type of retroperitoneal sarcomas is liposarcoma, which are frequently diagnosed incidentally. Major treatment in retroperitoneal liposarcoma is extensive surgical resection. Because of the risk of local recurrence and metastasis after surgery, these patients should be followed up by multidiciplinary for a long time. Postoperative follow-up of the patients should be multidisciplinary.

Herein we presented our approach to a 72-year-old liposarcoma case, who was admitted without follow-up after the first ope- ration and was presented with a giant retro- peritoneal mass of 24 cm 16 years later. 

Keywords

• liposarcoma,recurrence,retroperitoneum

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