Solid pseudodopillary tumor of the pancreas in children

Year 2024, Volume: 49 Issue: 1, 224 - 228, 29.03.2024

Serhan Küpeli

https://doi.org/10.17826/cumj.1416835

Abstract

Solid pseudopapillary tumor of the pancreas (SPTP) is mostly seen in young women in the second and third decades of life; it is quite uncommon in children. In this review, to deal with the current medical experience with SPTP in pediatric age group was aimed. In childen, SPTP demonstrates different clinical features. Complete resection is curative in most patients. In children, the optimal surgical strategy for SPTP is still obscure. Instead of radical resections, limited pancreatic resections, such as enucleations, with negative surgical margins should be attempted. For unresectable or recurrent tumours, cisplatin-based chemotherapy might be considered.

Keywords

Solid pseudopapillary tumor of the pancreas, treatment, prognosis, children

Ethical Statement

Since the type of the manuscript is review, ethics committee approval is not required.

Çocuklarda pankreasın solid psödodopiller tümörü

Abstract

Pankreasın solid psödopapiller tümörü (SPTP) çoğunlukla yaşamın ikinci ve üçüncü dekadındaki genç kadınlarda görülür; çocuklarda oldukça nadirdir. Bu derlemede pediatrik yaş grubunda SPTP ile ilgili güncel tıbbi deneyimin ele alınması amaçlandı. Çocuklarda SPTP farklı klinik özellikler gösterir. Çoğu hastada tam rezeksiyon küratiftir. Çocuklarda SPTP için en uygun cerrahi strateji hala belirsizdir. Radikal rezeksiyon yerine, enükleasyon gibi cerrahi sınırı negatif olan sınırlı pankreas rezeksiyonu denenmelidir. Rezeke edilemeyen veya tekrarlayan tümörler için sisplatin bazlı kemoterapi düşünülebilir. SPTP'nin prognozu, lokal nüks ve metastaz olsa bile olumlu biyolojik özellikleri nedeniyle çok iyidir.

Keywords

Pankreasın solid psödopapiller tümörü, tedavi, prognoz, çocuklar

Ethical Statement

Yazı tipi derleme olduğundan etik kurul onayı gerekli değildir.

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