Rare Soft Tissue Localized Distal Femur Parachordoma: Case Presentation

Year 2011, , 2 - 3, 01.08.2011

Güray Toğral Murat Arıkan Fisun Ardıç Yükrük Fatih Eksioğlu Şafak Güngör

https://doi.org/10.5505/aot.2011.36854

Abstract

Parachordoma, also named as myoepithelioma, is a rare,non axially located soft tissue tumor histologically resembling chordoma. This rare entity is also named as extra axial chordoma, parachordoma and chordoma periphericum. Lesions are generally seen in male patients and located at the lower extremities. The primary treatment modality is surgery. Even this tumor is benign, it may show local aggressive potential. Late local recurrences can be expected and pulmoner metastases are seldom. In this case presentation, a rare parachordoma case located at the distal femur is evaluated.

Keywords

Parachordoma, distal femur, wide resection, histopathological findings

Nadir Görülen Femur Distal Yumuşak Doku Yerleşimli Parakordoma: Olgu Sunumu

Abstract

Parakordoma myoepitelyoma olarak da isimlendirilen aksiyel dışı yerleşimli histolojik olarak kordomaya benzeyen yumuşak dokuların son derece nadir görülen bir tümörüdür. Bu nadir tümör extra-axial kordoma, parakordoma ya da kordoma periferikum olarak da adlandırılmaktadır. Lezyonlar daha sıklıkla erkeklerde görülür. Alt ekstremite en sık görülen lokalizasyon bölgesidir. Tedavisi öncelikle cerrahidir. İyi huylu bir tümör olmasına rağmen lokal agresif bir davranış gösterebilmektedir. Geç rekürrens gösterebilmekle birlikte nadirde olsa akciğer metastazı yapma potensiyelleri vardır. Bu olguda uyluk distalinden kaynaklanan ve çok nadir görülen bir parakordoma olgusu incelenmiştir.

Keywords

Parakordoma, femur distali, geniş rezeksiyon, histopatolojik bulgular

References

• Dabska M. Parachordoma: a new clinicopathologic entity. Cancer 1977;40:1586-92
• Kinoshita G, Yasoshima H. Case report: fatal parachordoma.J Orthop Sci 2007;12:101-6
• Van Akkooi ACJ, Van Geel AN, Bessems JHJM, Bakker MA. Extra-axial parachordoma.
• J Bone Joint Surg 2006;88:1232-4
• Huang CC, Cheng SM. Clinical and radiological presentations of pelvic parachordoma. Rare Tumors 2012;4:e5
• Silverberg’s Principles and Practice of Surgical Pathology and Cytopathology. 4th ed, Philadelphia, Churchill Livingstone, 2006,395-6
• Çıkar Çatışması: Yok
• Clabeaux J, Hoinowski L, Valente A, Damron TA. Case report: parachordoma of soft tissues of the arm. Clin Orthop Relat Res 2008:466:1251-6
• Fisher C. Parachordoma exists—but what is it? Adv Anat Pathol. 2000;7:141-8
• Folbe AL, Agoff SN, Willis J, Weis SW. Parachordoma
• cytogenetically distinct from axial chordoma and extraskeletal myxoid chondrosarcoma. Am J Surg Pathol. 1999;23:1059-67
• Zhang J, Wang H, Cheng X, Wang M, Zhu Y. A case of parachordoma on the chest wall and literature review. J Cancer Res Ther 2013;9:114-7
• and 10. Guedes A, Barreto BG, Barreto LG et al. Metatstatic parachordoma. J Cutan Pathol 2009;36:270-3
• Fisher C, Miettinen M. Parachordoma: A clinicopathologic and immunohistochemical study of four cases of an unusual soft tissue neoplasm. Ann Diagn Pathol 1997;1:3-10
• Miettinen Gannon FH, Lackman R. Chordomalike soft tissue sarcoma in the leg: a light and electron microscopic and immunohistochemical study. Ultrastruct Pathol 1992;16:577-86
• Estrems Díaz V, Bertó Martí FX, Zarzuela Sánchez V, Cabanes Ferrer MI, Bru Pomer A. Parachordoma of soft tissues of the arm: a very rare tumour. Case Rep Orthop 2013;2013:252376