LARON SYNDROME: A CASE REPORT

Nil Ceren Mungan

LARON SYNDROME: A CASE REPORT

Abstract

Aim: The purpose of this case report is to define oral-dental findings of Laron Syndrome. Laron syndrome, is a very rare familiar disorder with autosomal recessive transition. Case Report: A 11-year-old patient applied to Marmara University Faculty of Dentistry for dental treatment. She had growth inadequacy, small face and high pitched voice which are among the symptoms of the syndrome. Materials and Methods: In the intraoral examination, decays and crowded teeth on the upper jaw were observed due to small sized maxilla. The patient also had gingival inflammation due to the poor oral hygiene. The restorations were made and the patient was informed about the oral hygiene behaviors. Clinical Findings: Patients with Laron Syndrome have severe postnatal growth failure and a low level insulin like growth factor- 1(IGF-1). Children have very high-pitched voice, saddle nose, delayed puberty and delayed onset of teething.

Keywords

Laron syndrome,growth hormone insensitivity

References

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Details

Primary Language

English

Subjects

Health Care Administration

Journal Section

Research Article

Authors

Nil Ceren Mungan This is me

Publication Date

October 2, 2017

Submission Date

August 10, 2017

Acceptance Date

-

Published in Issue

Year 2017 Volume: 3 Number: 2

IZ

https://izlik.org/JA94EA68MT

Cite

RIS / Bibtex

APA

Mungan, N. C. (2017). LARON SYNDROME: A CASE REPORT. Aydın Dental Journal, 3(2), 45-48. https://izlik.org/JA94EA68MT

AMA

1.Mungan NC. LARON SYNDROME: A CASE REPORT. Aydin Dental Journal. 2017;3(2):45-48. https://izlik.org/JA94EA68MT

Chicago

Mungan, Nil Ceren. 2017. “LARON SYNDROME: A CASE REPORT”. Aydın Dental Journal 3 (2): 45-48. https://izlik.org/JA94EA68MT.

EndNote

Mungan NC (October 1, 2017) LARON SYNDROME: A CASE REPORT. Aydın Dental Journal 3 2 45–48.

IEEE

[1]N. C. Mungan, “LARON SYNDROME: A CASE REPORT”, Aydin Dental Journal, vol. 3, no. 2, pp. 45–48, Oct. 2017, [Online]. Available: https://izlik.org/JA94EA68MT

ISNAD

Mungan, Nil Ceren. “LARON SYNDROME: A CASE REPORT”. Aydın Dental Journal 3/2 (October 1, 2017): 45-48. https://izlik.org/JA94EA68MT.

JAMA

1.Mungan NC. LARON SYNDROME: A CASE REPORT. Aydin Dental Journal. 2017;3:45–48.

MLA

Mungan, Nil Ceren. “LARON SYNDROME: A CASE REPORT”. Aydın Dental Journal, vol. 3, no. 2, Oct. 2017, pp. 45-48, https://izlik.org/JA94EA68MT.

Vancouver

1.Nil Ceren Mungan. LARON SYNDROME: A CASE REPORT. Aydin Dental Journal [Internet]. 2017 Oct. 1;3(2):45-8. Available from: https://izlik.org/JA94EA68MT