Dev mezenterik iyi diferansiye liposarkoma bağlı ölüm: Olgu sunumu

Abstract

Liposarkomlar yetişkinlikte görülen en sık mezenkimal tümörler olmasına rağmen, primer mezenterik liposarkomlar oldukça nadirdir ve lokalizasyon, iyi diferansiye liposarkomlarda en önemli prognostik faktördür. Mezenter liposarkomlar için nadir bir lokalizasyondur.Ayakta şişlik şikayeti olan 50 yaşında erkek tetkikler devam ederken evinde rahatsızlandığı ve hastaneye götürülürken öldüğü belirtilmiştir. Otopsisinde, karın boşluğunda büyük mezenterik bir kitle saptanmıştır. Kitlenin kesit yüzü sarı-beyaz renkli, solid ve balık eti kıvamında olup düzensiz sınırlı, yama şeklinde sarı renkli nekrotik ve hemorajik alanlar içermektedir.Bu olgu 12000 gram ağırlığında büyük bir kitle ve nadir bir lokalizasyonda olmasından dolayı ilginç bulunarak mezenterik atypic lipomatous tumor/iyi diferansiye liposarkoma ALT/İDL bağlı ölüm olarak sunulmuştur.

Keywords

• Liposarkom
• mezenkimal tümör
• mezenter

Death related to huge mesenteric atypic lipomatous tumor/ well differentiated liposarcoma: Case Report

Abstract

Although liposarcomas are one of the most common mesenchymal tumors of adulthood, primary mesenteric liposarcomas are very rare and localization is the most important prognostic factor of atypic lipomatous tumor/well differentiated liposarcomas. Mesentery is a rare localization for liposarcomas.A case of a 50 years old man with swelling of leg is reported in this paper. During the investigation, his health condition got worse at home and died while being transferred to hospital. At autopsy; there were huge mesenteric mass in the abdominal cavity. Cut surface of mass was deep yellow to ivory in color, solid and fish-meat consistency and contain patches of yellow irregular necrotic and hemorrhagic areas.In this case, we report a death related with rare huge mesenteric atypic lipomatous tumor/well differentiated liposarcoma which is 12000 g in weight.

Keywords

• Liposarcoma
• mesenchymal tumor
• mesentery

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