RARE ORAL FINDINGS OF A PEDIATRIC PATIENT WITH PARRY ROMBERG SYNDROME: A CASE REPORT

Year 2024, Volume: 13 Issue: 1, 155 - 160, 26.01.2024

Derya Sarıoğlu , Özge Anıl

https://doi.org/10.54617/adoklinikbilimler.1284842

Abstract

Scleroderma is a chronic disease that causes thickening and hardening of the skin and subcutaneous tissues, resulting from disorders in collagen production and destruction. The most common type of scleroderma in children, which has many subtypes; is the linear form of localized scleroderma, in other words, morphea. Morphea; When it affects the jaw area, it can cause skeletal and dental orthodontic malformations and tooth eruption delays. Morphea; The form with progressive hemifacial atrophy that can progress to the skin, subcutaneous tissues and bone is called Parry Romberg Syndrome. Parry Romberg syndrome is a neurocutaneous disorder. In this case report, rare extraoral and intraoral findings in a pediatric patient with Parry Romberg Syndrome are discussed.

Keywords

localized scleroderma , morphea , pedodontics

Project Number

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PARRY ROMBERG SENDROMLU PEDİATRİK BİR HASTANIN NADİR ORAL BULGULARI: BİR OLGU SUNUMU

Abstract

Skleroderma; kollajen yapım ve yıkımında ortaya çıkan bozukluklardan kaynaklanan, deri ve deri altı dokularda kalınlaşmaya ve sertleşmeye yol açan kronik bir hastalıktır. Pek çok alt tipi olan sklerodermanın çocuklarda en çok görülen tipi; lokalize sklerodermanın lineer formu, diğer bir deyişle morfeadır. Morfea; çene bölgesini etkilediği zaman, iskeletsel ve dişsel ortodontik malformasyonlara ve dişlerde sürme gecikmelerine neden olabilmektedir. Morfeanın; deri, deri altı dokulara ve kemiğe kadar ilerleyebilen progresif hemifasial atrofiyle seyreden formuna Parry Romberg Sendromu adı verilir. Parry Romberg sendromu nörokutanoz bir rahatsızlıktır. Bu vaka sunumunda, Parry Romberg Sendromu’na sahip pediatrik bir hastada görülen, nadir ekstraoral ve intraoral bulgulardan bahsedilmiştir.

Keywords

lokalize skleroderma , morfea , pedodonti

Supporting Institution

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Project Number

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Thanks

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