A case of schizencephaly

Year 2013, Volume: 7 Issue: 1, 65 - 67, 01.10.2013

Ozan Turamanlar Oğuz Kırpıko Alpay Haktanır Oğuz Aslan Özen

https://doi.org/10.2399/ana.11.202

Abstract

Schizencephaly is a rare congenital disorder of cerebral cortical development. It is a neuronal migration anomaly, caused byinsults to migrating neuroblasts during 3rd to 5th gestational months. We encountered schizencephaly in the cranial magnetic resonance imaging (MRI) of a 4 month-old male baby. MRI demonstrated wide clefts occupying parietal regions bilaterally and the right occipital region partly. These areas were connected with lateral ventricles and also filled with cerebrospinal fluid. Although prevalence of this disorder is quite low and its incidence is unknown and also there may be no clearsymptoms as in our case, we emphasize that it should not be overlooked in differential diagnosis

Keywords

cranial, MRI, neurodevelopment anomaly, schizencephaly

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